KEGG 00280 Valine, leucine and isoleucine degradation
[list]

Species hsa(Human) mmu(Mouse) rno(Rat) gga(Chicken) dre(Zebrafish) dme(Fly) cel(Nematoda) mcc(Monkey) cfa(Dog) sce(Budding yeast) spo(Fission yeast) fca(Domestic cat)
UMAP
Representative coexpressed gene network LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
hsa00280 Valine, leucine and isoleucine degradation 31
hsa00071 Fatty acid degradation 15
hsa00640 Propanoate metabolism 14
hsa01200 Carbon metabolism 12
hsa01212 Fatty acid metabolism 11
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
mmu00280 Valine, leucine and isoleucine degradation 41
mmu00071 Fatty acid degradation 20
mmu01212 Fatty acid metabolism 17
mmu00640 Propanoate metabolism 15
mmu00380 Tryptophan metabolism 14
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
rno00280 Valine, leucine and isoleucine degradation 39
rno00071 Fatty acid degradation 20
rno01212 Fatty acid metabolism 17
rno00640 Propanoate metabolism 15
rno00380 Tryptophan metabolism 15
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
gga00280 Valine, leucine and isoleucine degradation 36
gga00640 Propanoate metabolism 14
gga00071 Fatty acid degradation 14
gga01212 Fatty acid metabolism 13
gga00380 Tryptophan metabolism 12
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
dre00280 Valine, leucine and isoleucine degradation 49
dre00071 Fatty acid degradation 31
dre01212 Fatty acid metabolism 20
dre00380 Tryptophan metabolism 19
dre00310 Lysine degradation 17
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
dme00280 Valine, leucine and isoleucine degradation 25
dme00071 Fatty acid degradation 16
dme00410 beta-Alanine metabolism 10
dme00640 Propanoate metabolism 9
dme01212 Fatty acid metabolism 9
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
cel00280 Valine, leucine and isoleucine degradation 35
cel00071 Fatty acid degradation 20
cel01212 Fatty acid metabolism 20
cel00640 Propanoate metabolism 14
cel00310 Lysine degradation 13
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
mcc00280 Valine, leucine and isoleucine degradation 33
mcc00640 Propanoate metabolism 15
mcc00071 Fatty acid degradation 14
mcc00650 Butanoate metabolism 12
mcc01212 Fatty acid metabolism 12
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
cfa00280 Valine, leucine and isoleucine degradation 30
cfa01212 Fatty acid metabolism 13
cfa00640 Propanoate metabolism 12
cfa01200 Carbon metabolism 12
cfa00071 Fatty acid degradation 12
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
sce00280 Valine, leucine and isoleucine degradation 6
sce00900 Terpenoid backbone biosynthesis 5
sce00770 Pantothenate and CoA biosynthesis 5
sce00071 Fatty acid degradation 4
sce00310 Lysine degradation 4
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
spo00280 Valine, leucine and isoleucine degradation 2
spo00650 Butanoate metabolism 2
spo00900 Terpenoid backbone biosynthesis 2
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
fca00280 Valine, leucine and isoleucine degradation 32
fca00071 Fatty acid degradation 16
fca01212 Fatty acid metabolism 14
fca00640 Propanoate metabolism 13
fca01200 Carbon metabolism 11
Gene list in the network
Symbol Function*
ABAT 4-aminobutyrate aminotransferase
ACAA1 acetyl-CoA acyltransferase 1
ACADM acyl-CoA dehydrogenase medium chain
ACADSB acyl-CoA dehydrogenase short/branched chain
ACAT1 acetyl-CoA acetyltransferase 1
ACAT2 acetyl-CoA acetyltransferase 2
ACO1 aconitase 1
AGL amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase
ALDH1B1 aldehyde dehydrogenase 1 family member B1
ALDH9A1 aldehyde dehydrogenase 9 family member A1
ATP5F1A ATP synthase F1 subunit alpha
ALDH7A1 aldehyde dehydrogenase 7 family member A1
BCKDHA branched chain keto acid dehydrogenase E1 subunit alpha
BCKDHB branched chain keto acid dehydrogenase E1 subunit beta
SLC25A20 solute carrier family 25 member 20
DBT dihydrolipoamide branched chain transacylase E2
DLD dihydrolipoamide dehydrogenase
ECH1 enoyl-CoA hydratase 1
ECHS1 enoyl-CoA hydratase, short chain 1
EHHADH enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
ETFDH electron transfer flavoprotein dehydrogenase
FDFT1 farnesyl-diphosphate farnesyltransferase 1
FDPS farnesyl diphosphate synthase
FH fumarate hydratase
HADHA hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
HADHB hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
HADH hydroxyacyl-CoA dehydrogenase
HMGCL 3-hydroxy-3-methylglutaryl-CoA lyase
HMGCS1 3-hydroxy-3-methylglutaryl-CoA synthase 1
IVD isovaleryl-CoA dehydrogenase
ALDH6A1 aldehyde dehydrogenase 6 family member A1
MMUT methylmalonyl-CoA mutase
OXCT1 3-oxoacid CoA-transferase 1
PCCA propionyl-CoA carboxylase subunit alpha
PCCB propionyl-CoA carboxylase subunit beta
PHYH phytanoyl-CoA 2-hydroxylase
SUCLG2 succinate-CoA ligase GDP-forming subunit beta
ACAA2 acetyl-CoA acyltransferase 2
ECI2 enoyl-CoA delta isomerase 2
HIBADH 3-hydroxyisobutyrate dehydrogenase
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
DHTKD1 dehydrogenase E1 and transketolase domain containing 1
MCCC1 methylcrotonyl-CoA carboxylase subunit 1
MCCC2 methylcrotonyl-CoA carboxylase subunit 2
ATPAF1 ATP synthase mitochondrial F1 complex assembly factor 1
CLYBL citramalyl-CoA lyase
Symbol Function*
Acadm acyl-Coenzyme A dehydrogenase, medium chain
Acadvl acyl-Coenzyme A dehydrogenase, very long chain
Acads acyl-Coenzyme A dehydrogenase, short chain
Aldh3a2 aldehyde dehydrogenase family 3, subfamily A2
Aox1 aldehyde oxidase 1
Bcat2 branched chain aminotransferase 2, mitochondrial
Bckdha branched chain ketoacid dehydrogenase E1, alpha polypeptide
Bckdhb branched chain ketoacid dehydrogenase E1, beta polypeptide
Cpt1a carnitine palmitoyltransferase 1a, liver
Cyp51 cytochrome P450, family 51
Dbt dihydrolipoamide branched chain transacylase E2
Gstz1 glutathione transferase zeta 1 (maleylacetoacetate isomerase)
Hadh hydroxyacyl-Coenzyme A dehydrogenase
Hsd17b10 hydroxysteroid (17-beta) dehydrogenase 10
Hmgcl 3-hydroxy-3-methylglutaryl-Coenzyme A lyase
Hmgcs2 3-hydroxy-3-methylglutaryl-Coenzyme A synthase 2
Rida reactive intermediate imine deaminase A homolog
Hsd17b4 hydroxysteroid (17-beta) dehydrogenase 4
Idh1 isocitrate dehydrogenase 1 (NADP+), soluble
Mmut methylmalonyl-Coenzyme A mutase
Suclg2 succinate-Coenzyme A ligase, GDP-forming, beta subunit
Ech1 enoyl coenzyme A hydratase 1, peroxisomal
Acaa2 acetyl-Coenzyme A acyltransferase 2 (mitochondrial 3-oxoacyl-Coenzyme A thiolase)
Nit2 nitrilase family, member 2
Ivd isovaleryl coenzyme A dehydrogenase
Aldh9a1 aldehyde dehydrogenase 9, subfamily A1
Hibadh 3-hydroxyisobutyrate dehydrogenase
Etfdh electron transferring flavoprotein, dehydrogenase
Acadsb acyl-Coenzyme A dehydrogenase, short/branched chain
Pccb propionyl Coenzyme A carboxylase, beta polypeptide
Acad8 acyl-Coenzyme A dehydrogenase family, member 8
Retsat retinol saturase (all trans retinol 13,14 reductase)
Bphl biphenyl hydrolase-like (serine hydrolase, breast epithelial mucin-associated antigen)
Clybl citrate lyase beta like
Aox3 aldehyde oxidase 3
Bdh1 3-hydroxybutyrate dehydrogenase, type 1
Mccc1 methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)
Aldh1b1 aldehyde dehydrogenase 1 family, member B1
Mcee methylmalonyl CoA epimerase
Ehhadh enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenase
Adhfe1 alcohol dehydrogenase, iron containing, 1
Mccc2 methylcrotonoyl-Coenzyme A carboxylase 2 (beta)
Aacs acetoacetyl-CoA synthetase
Echs1 enoyl Coenzyme A hydratase, short chain, 1, mitochondrial
Sfxn2 sideroflexin 2
Hadha hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
Aldh6a1 aldehyde dehydrogenase family 6, subfamily A1
Acat1 acetyl-Coenzyme A acetyltransferase 1
Acat2 acetyl-Coenzyme A acetyltransferase 2
Aldh7a1 aldehyde dehydrogenase family 7, member A1
Pcca propionyl-Coenzyme A carboxylase, alpha polypeptide
Etfa electron transferring flavoprotein, alpha polypeptide
Acaa1a acetyl-Coenzyme A acyltransferase 1A
Hmgcs1 3-hydroxy-3-methylglutaryl-Coenzyme A synthase 1
Vwa8 von Willebrand factor A domain containing 8
Hibch 3-hydroxyisobutyryl-Coenzyme A hydrolase
Kyat3 kynurenine aminotransferase 3
Hadhb hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
Acaa1b acetyl-Coenzyme A acyltransferase 1B
Acsf3 acyl-CoA synthetase family member 3
Abat 4-aminobutyrate aminotransferase
Idh2 isocitrate dehydrogenase 2 (NADP+), mitochondrial
Gcdh glutaryl-Coenzyme A dehydrogenase
Symbol Function*
Acaa1a acetyl-CoA acyltransferase 1A
Acadm acyl-CoA dehydrogenase medium chain
Hmgcs2 3-hydroxy-3-methylglutaryl-CoA synthase 2
Ivd isovaleryl-CoA dehydrogenase
Pccb propionyl-CoA carboxylase subunit beta
Acat1 acetyl-CoA acetyltransferase 1
Bckdha branched chain keto acid dehydrogenase E1 subunit alpha
Acadvl acyl-CoA dehydrogenase, very long chain
Cyp51 cytochrome P450, family 51
Scp2 sterol carrier protein 2
Acadsb acyl-CoA dehydrogenase, short/branched chain
Cpt1a carnitine palmitoyltransferase 1A
Aldh2 aldehyde dehydrogenase 2 family member
Dbt dihydrolipoamide branched chain transacylase E2
Hmgcs1 3-hydroxy-3-methylglutaryl-CoA synthase 1
Bckdhb branched chain keto acid dehydrogenase E1 subunit beta
Aox1 aldehyde oxidase 1
Hsd17b10 hydroxysteroid (17-beta) dehydrogenase 10
Hibadh 3-hydroxyisobutyrate dehydrogenase
Aldh9a1 aldehyde dehydrogenase 9 family, member A1
Bcat2 branched chain amino acid transaminase 2
Acads acyl-CoA dehydrogenase short chain
Decr2 2,4-dienoyl-CoA reductase 2
Ech1 enoyl-CoA hydratase 1
Aldh3a2 aldehyde dehydrogenase 3 family, member A2
Aacs acetoacetyl-CoA synthetase
Hmgcl 3-hydroxy-3-methylglutaryl-CoA lyase
Hsd17b4 hydroxysteroid (17-beta) dehydrogenase 4
Lss lanosterol synthase
Aldh6a1 aldehyde dehydrogenase 6 family, member A1
Mvd mevalonate diphosphate decarboxylase
Suox sulfite oxidase
Nfs1 NFS1 cysteine desulfurase
Pecr peroxisomal trans-2-enoyl-CoA reductase
Hadh hydroxyacyl-CoA dehydrogenase
Slc25a20 solute carrier family 25 member 20
Decr1 2,4-dienoyl-CoA reductase 1
Echs1 enoyl-CoA hydratase, short chain 1
Msmo1 methylsterol monooxygenase 1
Acaa2 acetyl-CoA acyltransferase 2
Hadha hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
Gcsh glycine cleavage system protein H
Ehhadh enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
Hadhb hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
Mtarc2 mitochondrial amidoxime reducing component 2
Nqo2 N-ribosyldihydronicotinamide:quinone reductase 2
Zadh2 zinc binding alcohol dehydrogenase, domain containing 2
Aldh7a1 aldehyde dehydrogenase 7 family, member A1
Etfb electron transfer flavoprotein subunit beta
Mcee methylmalonyl CoA epimerase
Mccc1 methylcrotonyl-CoA carboxylase subunit 1
Etfdh electron transfer flavoprotein dehydrogenase
Fahd2a fumarylacetoacetate hydrolase domain containing 2A
Gstk1 glutathione S-transferase kappa 1
Hibch 3-hydroxyisobutyryl-CoA hydrolase
Ldhd lactate dehydrogenase D
Acat2 acetyl-CoA acetyltransferase 2
Dhtkd1 dehydrogenase E1 and transketolase domain containing 1
Echdc1 ethylmalonyl-CoA decarboxylase 1
Idh2 isocitrate dehydrogenase (NADP(+)) 2
Mccc2 methylcrotonyl-CoA carboxylase subunit 2
Suclg2 succinate-CoA ligase GDP-forming subunit beta
Zfyve21 zinc finger FYVE-type containing 21
Tcaim T cell activation inhibitor, mitochondrial
Iba57 iron-sulfur cluster assembly factor IBA57
Gcdh glutaryl-CoA dehydrogenase
Nadk2 NAD kinase 2, mitochondrial
Acad8 acyl-CoA dehydrogenase family, member 8
Aox3 aldehyde oxidase 3
Acaa1b acetyl-Coenzyme A acyltransferase 1B
Kyat3 kynurenine aminotransferase 3
Aldh4a1 aldehyde dehydrogenase 4 family, member A1
Pcca propionyl-CoA carboxylase subunit alpha
Mmut methylmalonyl-CoA mutase
Symbol Function*
ATP5F1AZ ATP synthase F1 subunit alpha Z chromosome
BCKDHA branched chain keto acid dehydrogenase E1, alpha polypeptide
HMGCR 3-hydroxy-3-methylglutaryl-CoA reductase
DBT dihydrolipoamide branched chain transacylase E2
BCKDHB branched chain keto acid dehydrogenase E1 subunit beta
HSD17B4 hydroxysteroid 17-beta dehydrogenase 4
HADHA hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
HMGCL 3-hydroxy-3-methylglutaryl-CoA lyase
HMGCS1 3-hydroxy-3-methylglutaryl-CoA synthase 1
MCEE methylmalonyl-CoA epimerase
AACS acetoacetyl-CoA synthetase
ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain
ACOX1 acyl-CoA oxidase 1
ALDH3A2 aldehyde dehydrogenase 3 family member A2
DLD dihydrolipoamide dehydrogenase
GATD3A glutamine amidotransferase like class 1 domain containing 3A
PCCA propionyl-CoA carboxylase alpha subunit
CLYBL citrate lyase beta like
ACAT1 acetyl-CoA acetyltransferase 1
ECHDC3 enoyl-CoA hydratase domain containing 3
ALDH4A1 aldehyde dehydrogenase 4 family member A1
ACAD8 acyl-CoA dehydrogenase family member 8
HADH hydroxyacyl-CoA dehydrogenase
IDI2 isopentenyl-diphosphate delta isomerase 2
HIBADH 3-hydroxyisobutyrate dehydrogenase
ACAT2 acetyl-CoA acetyltransferase 2
HADHB hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit
MUT methylmalonyl-CoA mutase
MSMO1 methylsterol monooxygenase 1
IVD isovaleryl-CoA dehydrogenase
ALDH6A1 aldehyde dehydrogenase 6 family member A1
CISD1 CDGSH iron sulfur domain 1
ACADSB acyl-CoA dehydrogenase, short/branched chain
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
ACADL acyl-CoA dehydrogenase, long chain
COQ10B coenzyme Q10B
AOX1 aldehyde oxidase 1
AOX2 aldehyde oxidase 2
ALDH9A1 aldehyde dehydrogenase 9 family member A1
MCCC1 methylcrotonoyl-CoA carboxylase 1
HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10
DHTKD1 dehydrogenase E1 and transketolase domain containing 1
CSAD cysteine sulfinic acid decarboxylase
ADPRHL ADP-ribosylarginine hydrolase-like
PHYH phytanoyl-CoA 2-hydroxylase
ALDH7A1 aldehyde dehydrogenase 7 family member A1
GRAMD3 GRAM domain containing 3
ACAA2 acetyl-CoA acyltransferase 2
UQCRC2 ubiquinol-cytochrome c reductase core protein II
OXCT1 3-oxoacid CoA-transferase 1
NNT nicotinamide nucleotide transhydrogenase
NMRK1 nicotinamide riboside kinase 1
AUH AU RNA binding methylglutaconyl-CoA hydratase
MCCC2 methylcrotonoyl-CoA carboxylase 2
ACSF3 acyl-CoA synthetase family member 3
VWA8 von Willebrand factor A domain containing 8
PCCB propionyl-CoA carboxylase beta subunit
ACAA1 acetyl-CoA acyltransferase 1
ECHS1 enoyl-CoA hydratase, short chain 1
LOC100857197 uncharacterized LOC100857197
NDUFS2 NADH:ubiquinone oxidoreductase core subunit S2
PAOX polyamine oxidase
HSDL2 hydroxysteroid dehydrogenase like 2
ECH1 enoyl-CoA hydratase 1
GCAT glycine C-acetyltransferase
Symbol Function*
cat catalase
acat2 acetyl-CoA acetyltransferase 2
aldob aldolase b, fructose-bisphosphate
aldh3a2a aldehyde dehydrogenase 3 family, member A2a
eci1 enoyl-CoA delta isomerase 1
aldh7a1 aldehyde dehydrogenase 7 family, member A1
hadhb hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
aldh2.2 aldehyde dehydrogenase 2 family member, tandem duplicate 2
ivd isovaleryl-CoA dehydrogenase
echs1 enoyl CoA hydratase, short chain, 1, mitochondrial
glud1b glutamate dehydrogenase 1b
aifm1 apoptosis inducing factor mitochondrion associated 1
acad11 acyl-CoA dehydrogenase family, member 11
ociad1 OCIA domain containing 1
aldh2.1 aldehyde dehydrogenase 2 family member, tandem duplicate 1
pdhx pyruvate dehydrogenase complex component X
uqcrc1 ubiquinol-cytochrome c reductase core protein 1
fh fumarate hydratase
sigmar1 sigma non-opioid intracellular receptor 1
aacs acetoacetyl-CoA synthetase
hmgcs1 3-hydroxy-3-methylglutaryl-CoA synthase 1 (soluble)
acad8 acyl-CoA dehydrogenase family, member 8
hibadhb 3-hydroxyisobutyrate dehydrogenase b
acadl acyl-CoA dehydrogenase long chain
hmgcl 3-hydroxy-3-methylglutaryl-CoA lyase
dldh dihydrolipoamide dehydrogenase
aldh9a1b aldehyde dehydrogenase 9 family, member A1b
gcat glycine C-acetyltransferase
adh8b alcohol dehydrogenase 8b
pccb propionyl-CoA carboxylase subunit beta
mccc2 methylcrotonyl-CoA carboxylase subunit 2
etfb electron transfer flavoprotein subunit beta
acadm acyl-CoA dehydrogenase medium chain
acaa2 acetyl-CoA acyltransferase 2
acaa1 acetyl-CoA acyltransferase 1
aldh6a1 aldehyde dehydrogenase 6 family, member A1
decr1 2,4-dienoyl CoA reductase 1, mitochondrial
eci2 enoyl-CoA delta isomerase 2
bcat2 branched chain amino-acid transaminase 2, mitochondrial
phb2b prohibitin 2b
pcca propionyl-CoA carboxylase subunit alpha
oxct1a 3-oxoacid CoA transferase 1a
hadh hydroxyacyl-CoA dehydrogenase
auh AU RNA binding protein/enoyl-CoA hydratase
hibadha 3-hydroxyisobutyrate dehydrogenase a
acads acyl-CoA dehydrogenase short chain
acat1 acetyl-CoA acetyltransferase 1
etfdh electron transfer flavoprotein dehydrogenase
park7 parkinson protein 7
cpt1b carnitine palmitoyltransferase 1B (muscle)
zgc:101569 zgc:101569
hsd17b10 hydroxysteroid (17-beta) dehydrogenase 10
aldh16a1 aldehyde dehydrogenase 16 family, member A1
ndufs1 NADH:ubiquinone oxidoreductase core subunit S1
ndufa9a NADH:ubiquinone oxidoreductase subunit A9a
dbt dihydrolipoamide branched chain transacylase E2
fdps farnesyl diphosphate synthase (farnesyl pyrophosphate synthetase, dimethylallyltranstransferase, geranyltranstransferase)
hadhaa hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha a
atp5fa1 ATP synthase F1 subunit alpha
mcee methylmalonyl CoA epimerase
bckdha branched chain keto acid dehydrogenase E1 subunit alpha
atp5f1b ATP synthase F1 subunit beta
cpt1ab carnitine palmitoyltransferase 1Ab (liver)
acsf3 acyl-CoA synthetase family member 3
gstr glutathione S-transferase rho
l2hgdh L-2-hydroxyglutarate dehydrogenase
mmut methylmalonyl CoA mutase
bckdhb branched chain keto acid dehydrogenase E1 subunit beta
aox6 aldehyde oxidase 6
zgc:162816 zgc:162816
acadvl acyl-CoA dehydrogenase very long chain
acsf2 acyl-CoA synthetase family member 2
mccc1 methylcrotonyl-CoA carboxylase subunit
retsat.1 retinol saturase, tandem duplicate 1
hadhab hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha b
lss lanosterol synthase (2,3-oxidosqualene-lanosterol cyclase)
hibch 3-hydroxyisobutyryl-CoA hydrolase
ehhadh enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase
si:ch211-198n5.11 si:ch211-198n5.11
aldh9a1a.1 aldehyde dehydrogenase 9 family, member A1a, tandem duplicate 1
cpt2 carnitine palmitoyltransferase 2
aldh9a1a.2 aldehyde dehydrogenase 9 family, member A1a, tandem duplicate 2
LOC100037342 acyl-CoA dehydrogenase, short/branched chain-like
wu:fb14d09 wu:fb14d09
acadsb acyl-CoA dehydrogenase short/branched chain
Symbol Function*
CG17896 uncharacterized protein
CG10932 uncharacterized protein
CG1673 uncharacterized protein
Lsd-2 Lipid storage droplet-2
CG5599 uncharacterized protein
scu scully
CG9577 uncharacterized protein
CG12512 uncharacterized protein
CG9547 uncharacterized protein
Hmgcl 3-Hydroxymethyl-3-methylglutaryl-CoA lyase
Aldh Aldehyde dehydrogenase
Mtpalpha Mitochondrial trifunctional protein alpha subunit
yip2 yippee interacting protein 2
CG4598 uncharacterized protein
CG4594 uncharacterized protein
CG10194 uncharacterized protein
Etf-QO Electron transfer flavoprotein-ubiquinone oxidoreductase
Echs1 Enoyl-CoA hydratase, short chain 1
CG8311 uncharacterized protein
CG6984 uncharacterized protein
CG15093 uncharacterized protein
l(2)k09913 lethal (2) k09913
Mtpbeta Mitochondrial trifunctional protein beta subunit
SCOT Succinyl-CoA:3-ketoacid CoA transferase
PHGPx PHGPx
Mcad Medium-chain acyl-CoA dehydrogenase
CG6638 uncharacterized protein
CG3902 uncharacterized protein
Aldh7A1 Aldehyde dehydrogenase 7 family member A1
CG11241 uncharacterized protein
CG8199 uncharacterized protein
Fdh Formaldehyde dehydrogenase
CG4860 uncharacterized protein
CG7530 uncharacterized protein
CG5044 uncharacterized protein
CG6126 uncharacterized protein
Arc42 Arc42
CG31075 uncharacterized protein
CG5590 uncharacterized protein
CROT Carnitine O-octanoyltransferase
CG7834 uncharacterized protein
Mccc1 Methylcrotonoyl-CoA carboxylase 1
Mccc2 Methylcrotonoyl-CoA carboxylase 2
CG31548 uncharacterized protein
Symbol Function*
ech-1.2 Enoyl-CoA Hydratase
acdh-3 Acyl CoA DeHydrogenase
acdh-1 Acyl CoA DeHydrogenase
bckd-1B Transket_pyr domain-containing protein
ech-7 Enoyl-CoA Hydratase
acdh-9 Acyl CoA DeHydrogenase
pod-2 Acetyl-CoA carboxylase
Y25C1A.13 Uncharacterized protein
kat-1 Acetyl-CoA acetyltransferase homolog, mitochondrial
acdh-12 Acyl CoA DeHydrogenase
dbt-1 Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
ZK1320.9 Acetyl-CoA deacylase
C05C10.3 putative succinyl-CoA:3-ketoacid coenzyme A transferase, mitochondrial
gbh-1 putative gamma-butyrobetaine dioxygenase
ech-4 ACB domain-containing protein
nuo-1 NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial
F54D5.12 FAD-binding PCMH-type domain-containing protein
alh-8 putative methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
hphd-1 Hydroxyacid-oxoacid transhydrogenase, mitochondrial
F57C2.5 Adipocyte plasma membrane-associated protein;Str_synth domain-containing protein
pck-1 Phosphoenolpyruvate carboxykinase (GTP)
nduf-9 NmrA domain-containing protein
M01F1.4 Uncharacterized protein
gsr-1 Glutathione reductase, mitochondrial
mmcm-1 putative methylmalonyl-CoA mutase, mitochondrial
alh-1 Aldedh domain-containing protein
hach-1 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
F25B5.3 5'-nucleotidase;Putative cytosolic 5'-nucleotidase 3;Uncharacterized protein
let-721 Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial
B0303.3 putative 3-ketoacyl-CoA thiolase
ech-6 putative enoyl-CoA hydratase, mitochondrial
acdh-11 Acyl-CoA dehydrogenase family member 11
bckd-1A 2-oxoisovalerate dehydrogenase subunit alpha;2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
acaa-2 ACetyl-CoA Acyltransferase 2 homolog
ivd-1 Butyryl-CoA dehydrogenase
elo-5 Elongation of very long chain fatty acids protein 5
elo-6 Elongation of very long chain fatty acids protein 6
mccc-1 MethylCrotonoyl-Coenzyme A Carboxylase (alpha)
gta-1 putative 4-aminobutyrate aminotransferase, mitochondrial
ard-1 Alcohol/Ribitol Dehydrogenase family
gdh-1 Glutamate dehydrogenase
elo-2 Elongation of very long chain fatty acids protein
hacd-1 Hydroxy-Acyl-CoA Dehydrogenase
alh-5 Aldehyde dehydrogenase
exc-15 Aldo_ket_red domain-containing protein
alh-4 Aldehyde dehydrogenase
ech-1.1 Enoyl-CoA Hydratase
B0250.5 putative 3-hydroxyisobutyrate dehydrogenase, mitochondrial
dhs-25 DeHydrogenases, Short chain
pfk-1.1 ATP-dependent 6-phosphofructokinase 1
pccb-1 Propionyl Coenzyme A Carboxylase Beta subunit
K11G12.6 Lipase maturation factor
sur-5 Acetoacetyl-CoA synthetase
pcca-1 Propionyl-CoA carboxylase alpha chain, mitochondrial
B0272.3 putative 3-hydroxyacyl-CoA dehydrogenase B0272.3
idhb-1 putative isocitrate dehydrogenase [NAD] subunit beta, mitochondrial
acdh-7 Acyl CoA DeHydrogenase
cTel55X.1 Uncharacterized protein
C05D11.5 Putative hydroxypyruvate isomerase
alh-11 Aldedh domain-containing protein
T02G5.7 Uncharacterized protein
acdh-10 putative medium-chain specific acyl-CoA dehydrogenase 10, mitochondrial
F02A9.10 putative methylcrotonoyl-CoA carboxylase beta chain, mitochondrial
Symbol Function*
BTD biotinidase
PXMP2 peroxisomal membrane protein 2
GRHPR glyoxylate and hydroxypyruvate reductase
PBLD phenazine biosynthesis like protein domain containing
ALDH9A1 aldehyde dehydrogenase 9 family member A1
HADHA hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
DECR1 2,4-dienoyl-CoA reductase 1
PANK1 pantothenate kinase 1
HADH hydroxyacyl-CoA dehydrogenase
OXCT1 3-oxoacid CoA-transferase 1
ACAA1 acetyl-CoA acyltransferase 1
SUCLG2 succinate-CoA ligase GDP-forming subunit beta
UQCRC2 ubiquinol-cytochrome c reductase core protein II
PTGR2 prostaglandin reductase 2
HADHB hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
ACADS acyl-CoA dehydrogenase short chain
ALDH6A1 aldehyde dehydrogenase 6 family member A1
CLYBL citramalyl-CoA lyase
PCCA propionyl-CoA carboxylase subunit alpha
HSD17B10 hydroxysteroid 17-beta dehydrogenase 10
DLD dihydrolipoamide dehydrogenase
NNT nicotinamide nucleotide transhydrogenase
EHHADH enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
MCCC2 methylcrotonyl-CoA carboxylase subunit 2
HMGCS1 3-hydroxy-3-methylglutaryl-CoA synthase 1
ALDH7A1 aldehyde dehydrogenase 7 family member A1
AIFM1 apoptosis inducing factor mitochondria associated 1
HIBADH 3-hydroxyisobutyrate dehydrogenase
IVD isovaleryl-CoA dehydrogenase
ACADM acyl-CoA dehydrogenase medium chain
MMUT methylmalonyl-CoA mutase
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
AACS acetoacetyl-CoA synthetase
ACADSB acyl-CoA dehydrogenase short/branched chain
ACAT1 acetyl-CoA acetyltransferase 1
ETFA electron transfer flavoprotein subunit alpha
ALDH5A1 aldehyde dehydrogenase 5 family member A1
MCCC1 methylcrotonyl-CoA carboxylase subunit 1
ACAA2 acetyl-CoA acyltransferase 2
HMGCL 3-hydroxy-3-methylglutaryl-CoA lyase
NDUFV1 NADH:ubiquinone oxidoreductase core subunit V1
DBT dihydrolipoamide branched chain transacylase E2
FAH fumarylacetoacetate hydrolase
ALDH2 aldehyde dehydrogenase 2 family member
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
ABAT 4-aminobutyrate aminotransferase
SAMM50 SAMM50 sorting and assembly machinery component
FASN fatty acid synthase
PCCB propionyl-CoA carboxylase subunit beta
CAT catalase
NIPSNAP1 nipsnap homolog 1
BCKDHB branched chain keto acid dehydrogenase E1 subunit beta
ETFB electron transfer flavoprotein subunit beta
ECHS1 enoyl-CoA hydratase, short chain 1
VAT1 vesicle amine transport 1
BCKDHA branched chain keto acid dehydrogenase E1, alpha polypeptide
ACAD11 acyl-CoA dehydrogenase family member 11
Symbol Function*
DLD dihydrolipoamide dehydrogenase
HSD17B4 hydroxysteroid 17-beta dehydrogenase 4
MMUT methylmalonyl-CoA mutase
BCKDHB branched chain keto acid dehydrogenase E1 subunit beta
NDUFV1 NADH:ubiquinone oxidoreductase core subunit V1
AUH AU RNA binding methylglutaconyl-CoA hydratase
ETFB electron transfer flavoprotein subunit beta
PCCA propionyl-CoA carboxylase subunit alpha
ACAA1 acetyl-CoA acyltransferase 1
PCCB propionyl-CoA carboxylase subunit beta
ACADS acyl-CoA dehydrogenase short chain
NCOA4 nuclear receptor coactivator 4
ACADSB acyl-CoA dehydrogenase short/branched chain
DHTKD1 dehydrogenase E1 and transketolase domain containing 1
MECR mitochondrial trans-2-enoyl-CoA reductase
HADH hydroxyacyl-CoA dehydrogenase
SDHA succinate dehydrogenase complex flavoprotein subunit A
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
MCEE methylmalonyl-CoA epimerase
HMGCR 3-hydroxy-3-methylglutaryl-CoA reductase
HMGCS1 3-hydroxy-3-methylglutaryl-CoA synthase 1
OXCT1 3-oxoacid CoA-transferase 1
ACAD8 acyl-CoA dehydrogenase family member 8
HIBADH 3-hydroxyisobutyrate dehydrogenase
FDPS farnesyl diphosphate synthase
AIFM1 apoptosis inducing factor mitochondria associated 1
NSDHL NAD(P) dependent steroid dehydrogenase-like
ALDH7A1 aldehyde dehydrogenase 7 family member A1
PEX7 peroxisomal biogenesis factor 7
ACAT2 acetyl-CoA acetyltransferase 2
BCAT2 branched chain amino acid transaminase 2
BCKDHA branched chain keto acid dehydrogenase E1 subunit alpha
AACS acetoacetyl-CoA synthetase
EHHADH enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
ACAT1 acetyl-CoA acetyltransferase 1
ACADM acyl-CoA dehydrogenase medium chain
ACAA2 acetyl-CoA acyltransferase 2
ALDH6A1 aldehyde dehydrogenase 6 family member A1
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
ACLY ATP citrate lyase
HADHB hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
CLPX caseinolytic mitochondrial matrix peptidase chaperone subunit X
HMGCL 3-hydroxy-3-methylglutaryl-CoA lyase
IVD isovaleryl-CoA dehydrogenase
DLST dihydrolipoamide S-succinyltransferase
HADHA hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
Symbol Function*
ERG20 bifunctional (2E,6E)-farnesyl diphosphate synthase/dimethylallyltranstransferase
ILV3 dihydroxy-acid dehydratase ILV3
OAC1 Oac1p
ALD4 aldehyde dehydrogenase (NADP(+)) ALD4
ERG13 hydroxymethylglutaryl-CoA synthase
ERG12 mevalonate kinase
MVD1 diphosphomevalonate decarboxylase MVD1
ALD6 aldehyde dehydrogenase (NADP(+)) ALD6
ERG10 acetyl-CoA C-acetyltransferase
BAT1 branched-chain-amino-acid transaminase BAT1
ALD5 aldehyde dehydrogenase (NAD(P)(+)) ALD5
Symbol Function*
SPBC24C6.04 putative delta-1-pyrroline-5-carboxylate dehydrogenase
erg10 putative acetyl-CoA C-acetyltransferase Erg10
hcs1 3-hydroxy-3-methylglutaryl-CoA synthase
Symbol Function*
HIBADH 3-hydroxyisobutyrate dehydrogenase
BCKDHB branched chain keto acid dehydrogenase E1 subunit beta
PCCA propionyl-CoA carboxylase subunit alpha
MMUT methylmalonyl-CoA mutase
ACADS acyl-CoA dehydrogenase short chain
PCCB propionyl-CoA carboxylase subunit beta
GALNT11 polypeptide N-acetylgalactosaminyltransferase 11
EHHADH enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
HADHB hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
HADHA hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
NUDT13 nudix hydrolase 13
ETFB electron transfer flavoprotein subunit beta
ETFDH electron transfer flavoprotein dehydrogenase
MCEE methylmalonyl-CoA epimerase
POLDIP2 DNA polymerase delta interacting protein 2
ACAD9 acyl-CoA dehydrogenase family member 9
ALDH7A1 aldehyde dehydrogenase 7 family member A1
GCDH glutaryl-CoA dehydrogenase
BCKDHA branched chain keto acid dehydrogenase E1 subunit alpha
DBT dihydrolipoamide branched chain transacylase E2
GSTK1 glutathione S-transferase kappa 1
HADH hydroxyacyl-CoA dehydrogenase
ACADM acyl-CoA dehydrogenase medium chain
MRS2 magnesium transporter MRS2
ACAT1 acetyl-CoA acetyltransferase 1
TSTD1 thiosulfate sulfurtransferase like domain containing 1
ACAA2 acetyl-CoA acyltransferase 2
ECHS1 enoyl-CoA hydratase, short chain 1
IVD isovaleryl-CoA dehydrogenase
VWA8 von Willebrand factor A domain containing 8
MCCC2 methylcrotonyl-CoA carboxylase subunit 2
ALDH6A1 aldehyde dehydrogenase 6 family member A1
HMGCS1 3-hydroxy-3-methylglutaryl-CoA synthase 1
LOC101092274 acyl-coenzyme A thioesterase 1
ACADSB acyl-CoA dehydrogenase short/branched chain
NIT2 nitrilase family member 2
ECH1 enoyl-CoA hydratase 1
ACAT2 acetyl-CoA acetyltransferase 2
DLD dihydrolipoamide dehydrogenase
ACADVL acyl-CoA dehydrogenase very long chain
DLST dihydrolipoamide S-succinyltransferase
ETFA electron transfer flavoprotein subunit alpha
PPARA peroxisome proliferator activated receptor alpha
SPX spexin hormone
AUH AU RNA binding methylglutaconyl-CoA hydratase
ALDH3A2 aldehyde dehydrogenase 3 family member A2
MCCC1 methylcrotonyl-CoA carboxylase subunit 1
COQ5 coenzyme Q5, methyltransferase
PDSS2 decaprenyl diphosphate synthase subunit 2
ACAD8 acyl-CoA dehydrogenase family member 8
LOC101098145 dehydrogenase/reductase SDR family member 4
TCAIM T cell activation inhibitor, mitochondrial
HMGCR 3-hydroxy-3-methylglutaryl-CoA reductase
HMGCL 3-hydroxy-3-methylglutaryl-CoA lyase
EIF4EBP2 eukaryotic translation initiation factor 4E binding protein 2
ACSF3 acyl-CoA synthetase family member 3
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
TXNRD2 thioredoxin reductase 2
LOC102900295 uncharacterized LOC102900295
LOC102901899 isopentenyl-diphosphate Delta-isomerase 1
LOC111559111 3-ketoacyl-CoA thiolase, mitochondrial-like


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