KEGG 00190 Oxidative phosphorylation
[list]

Species hsa(Human) mmu(Mouse) rno(Rat) gga(Chicken) dre(Zebrafish) dme(Fly) cel(Nematoda) mcc(Monkey) cfa(Dog) sce(Budding yeast) spo(Fission yeast) fca(Domestic cat)
UMAP
Representative coexpressed gene network LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
hsa00190 Oxidative phosphorylation 95
hsa04714 Thermogenesis 80
hsa05016 Huntington disease 79
hsa05208 Chemical carcinogenesis - reactive oxygen species 78
hsa05012 Parkinson disease 77
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
mmu00190 Oxidative phosphorylation 104
mmu05012 Parkinson disease 82
mmu05016 Huntington disease 82
mmu05022 Pathways of neurodegeneration - multiple diseases 82
mmu05415 Diabetic cardiomyopathy 82
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
rno00190 Oxidative phosphorylation 105
rno04714 Thermogenesis 88
rno05016 Huntington disease 83
rno05415 Diabetic cardiomyopathy 83
rno05012 Parkinson disease 82
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
gga00190 Oxidative phosphorylation 88
gga01200 Carbon metabolism 18
gga04260 Cardiac muscle contraction 18
gga00020 Citrate cycle (TCA cycle) 15
gga04145 Phagosome 14
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
dre00190 Oxidative phosphorylation 114
dre04260 Cardiac muscle contraction 30
dre04145 Phagosome 21
dre01200 Carbon metabolism 19
dre00020 Citrate cycle (TCA cycle) 17
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
dme00190 Oxidative phosphorylation 95
dme04145 Phagosome 18
dme00020 Citrate cycle (TCA cycle) 12
dme01200 Carbon metabolism 12
dme04150 mTOR signaling pathway 10
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
cel00190 Oxidative phosphorylation 90
cel04145 Phagosome 17
cel01200 Carbon metabolism 15
cel00020 Citrate cycle (TCA cycle) 13
cel04142 Lysosome 9
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
mcc00190 Oxidative phosphorylation 90
mcc04714 Thermogenesis 82
mcc05012 Parkinson disease 78
mcc05016 Huntington disease 77
mcc05415 Diabetic cardiomyopathy 77
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
cfa00190 Oxidative phosphorylation 85
cfa05010 Alzheimer disease 71
cfa05016 Huntington disease 71
cfa05022 Pathways of neurodegeneration - multiple diseases 71
cfa05012 Parkinson disease 70
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
sce00190 Oxidative phosphorylation 57
sce04145 Phagosome 14
sce00020 Citrate cycle (TCA cycle) 7
sce01200 Carbon metabolism 7
sce00860 Porphyrin metabolism 2
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
spo00190 Oxidative phosphorylation 46
spo04145 Phagosome 12
spo00020 Citrate cycle (TCA cycle) 5
spo01200 Carbon metabolism 5
spo03018 RNA degradation 2
LCNkegg
KEGG* ID Title #genes Link to the KEGG* map
(Multiple genes)
fca00190 Oxidative phosphorylation 91
fca04714 Thermogenesis 80
fca05010 Alzheimer disease 76
fca05012 Parkinson disease 76
fca05014 Amyotrophic lateral sclerosis 76
Gene list in the network
Symbol Function*
ACO2 aconitase 2
ATOX1 antioxidant 1 copper chaperone
ATP5F1A ATP synthase F1 subunit alpha
ATP5F1B ATP synthase F1 subunit beta
ATP5F1C ATP synthase F1 subunit gamma
ATP5F1D ATP synthase F1 subunit delta
ATP5F1E ATP synthase F1 subunit epsilon
ATP5PB ATP synthase peripheral stalk-membrane subunit b
ATP5MC1 ATP synthase membrane subunit c locus 1
ATP5MC2 ATP synthase membrane subunit c locus 2
ATP5MC3 ATP synthase membrane subunit c locus 3
ATP5ME ATP synthase membrane subunit e
ATP5PF ATP synthase peripheral stalk subunit F6
ATP6V1A ATPase H+ transporting V1 subunit A
ATP6V1B2 ATPase H+ transporting V1 subunit B2
ATP6V0C ATPase H+ transporting V0 subunit c
ATP6V1C1 ATPase H+ transporting V1 subunit C1
ATP6V1E1 ATPase H+ transporting V1 subunit E1
ATP6V0B ATPase H+ transporting V0 subunit b
ATP6V0A1 ATPase H+ transporting V0 subunit a1
ATP6AP1 ATPase H+ transporting accessory protein 1
ATP5PO ATP synthase peripheral stalk subunit OSCP
COX4I1 cytochrome c oxidase subunit 4I1
COX5B cytochrome c oxidase subunit 5B
COX6A1 cytochrome c oxidase subunit 6A1
COX6B1 cytochrome c oxidase subunit 6B1
COX6C cytochrome c oxidase subunit 6C
COX7A2 cytochrome c oxidase subunit 7A2
COX7B cytochrome c oxidase subunit 7B
COX7C cytochrome c oxidase subunit 7C
COX8A cytochrome c oxidase subunit 8A
COX15 cytochrome c oxidase assembly homolog COX15
CYC1 cytochrome c1
DLAT dihydrolipoamide S-acetyltransferase
DLD dihydrolipoamide dehydrogenase
ECHS1 enoyl-CoA hydratase, short chain 1
ETFA electron transfer flavoprotein subunit alpha
GLRX glutaredoxin
HINT1 histidine triad nucleotide binding protein 1
IDH3B isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit beta
IDH3G isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit gamma
MDH1 malate dehydrogenase 1
MGST2 microsomal glutathione S-transferase 2
MGST3 microsomal glutathione S-transferase 3
NDUFA1 NADH:ubiquinone oxidoreductase subunit A1
NDUFA2 NADH:ubiquinone oxidoreductase subunit A2
NDUFA3 NADH:ubiquinone oxidoreductase subunit A3
NDUFA4 NDUFA4 mitochondrial complex associated
NDUFA5 NADH:ubiquinone oxidoreductase subunit A5
NDUFA6 NADH:ubiquinone oxidoreductase subunit A6
NDUFA7 NADH:ubiquinone oxidoreductase subunit A7
NDUFA8 NADH:ubiquinone oxidoreductase subunit A8
NDUFA9 NADH:ubiquinone oxidoreductase subunit A9
NDUFA10 NADH:ubiquinone oxidoreductase subunit A10
NDUFAB1 NADH:ubiquinone oxidoreductase subunit AB1
NDUFB1 NADH:ubiquinone oxidoreductase subunit B1
NDUFB2 NADH:ubiquinone oxidoreductase subunit B2
NDUFB3 NADH:ubiquinone oxidoreductase subunit B3
NDUFB4 NADH:ubiquinone oxidoreductase subunit B4
NDUFB5 NADH:ubiquinone oxidoreductase subunit B5
NDUFB6 NADH:ubiquinone oxidoreductase subunit B6
NDUFB7 NADH:ubiquinone oxidoreductase subunit B7
NDUFB8 NADH:ubiquinone oxidoreductase subunit B8
NDUFB9 NADH:ubiquinone oxidoreductase subunit B9
NDUFB10 NADH:ubiquinone oxidoreductase subunit B10
NDUFC1 NADH:ubiquinone oxidoreductase subunit C1
NDUFC2 NADH:ubiquinone oxidoreductase subunit C2
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
NDUFS2 NADH:ubiquinone oxidoreductase core subunit S2
NDUFS3 NADH:ubiquinone oxidoreductase core subunit S3
NDUFV1 NADH:ubiquinone oxidoreductase core subunit V1
NDUFS4 NADH:ubiquinone oxidoreductase subunit S4
NDUFS5 NADH:ubiquinone oxidoreductase subunit S5
NDUFS6 NADH:ubiquinone oxidoreductase subunit S6
NDUFS8 NADH:ubiquinone oxidoreductase core subunit S8
NDUFV2 NADH:ubiquinone oxidoreductase core subunit V2
NDUFV3 NADH:ubiquinone oxidoreductase subunit V3
PCCB propionyl-CoA carboxylase subunit beta
PDHA1 pyruvate dehydrogenase E1 subunit alpha 1
PDHB pyruvate dehydrogenase E1 subunit beta
PFKM phosphofructokinase, muscle
SLC25A3 solute carrier family 25 member 3
POLR2I RNA polymerase II subunit I
POLR2L RNA polymerase II, I and III subunit L
PPA1 inorganic pyrophosphatase 1
PEX19 peroxisomal biogenesis factor 19
SDHA succinate dehydrogenase complex flavoprotein subunit A
SDHB succinate dehydrogenase complex iron sulfur subunit B
SDHC succinate dehydrogenase complex subunit C
SDHD succinate dehydrogenase complex subunit D
SELENOW selenoprotein W
SOD1 superoxide dismutase 1
ELOB elongin B
TUFM Tu translation elongation factor, mitochondrial
UQCRB ubiquinol-cytochrome c reductase binding protein
UQCRC1 ubiquinol-cytochrome c reductase core protein 1
UQCRC2 ubiquinol-cytochrome c reductase core protein 2
UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
UQCRH ubiquinol-cytochrome c reductase hinge protein
VDAC2 voltage dependent anion channel 2
NAPA NSF attachment protein alpha
SUCLG1 succinate-CoA ligase GDP/ADP-forming subunit alpha
ATP6V0D1 ATPase H+ transporting V0 subunit d1
COX7A2L cytochrome c oxidase subunit 7A2 like
ATP6V1F ATPase H+ transporting V1 subunit F
COX5A cytochrome c oxidase subunit 5A
ATP6V1G1 ATPase H+ transporting V1 subunit G1
ATP5MF ATP synthase membrane subunit f
ATP5MJ ATP synthase membrane subunit j
RBX1 ring-box 1
COX17 cytochrome c oxidase copper chaperone COX17
BCAP31 B cell receptor associated protein 31
ATP5PD ATP synthase peripheral stalk subunit d
LAMTOR5 late endosomal/lysosomal adaptor, MAPK and MTOR activator 5
ATP5MG ATP synthase membrane subunit g
UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI
NNT nicotinamide nucleotide transhydrogenase
MTCH2 mitochondrial carrier 2
TIMM13 translocase of inner mitochondrial membrane 13
PPA2 inorganic pyrophosphatase 2
UQCRQ ubiquinol-cytochrome c reductase complex III subunit VII
CHMP2A charged multivesicular body protein 2A
EIF3K eukaryotic translation initiation factor 3 subunit K
C19orf53 chromosome 19 open reading frame 53
PHPT1 phosphohistidine phosphatase 1
UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X
NDUFA13 NADH:ubiquinone oxidoreductase subunit A13
CHCHD2 coiled-coil-helix-coiled-coil-helix domain containing 2
ATP6V1D ATPase H+ transporting V1 subunit D
WDR83OS WD repeat domain 83 opposite strand
CHMP5 charged multivesicular body protein 5
ATP6V1H ATPase H+ transporting V1 subunit H
CYCS cytochrome c, somatic
NDUFB11 NADH:ubiquinone oxidoreductase subunit B11
MRPL16 mitochondrial ribosomal protein L16
PLEKHB2 pleckstrin homology domain containing B2
NOP10 NOP10 ribonucleoprotein
PLGRKT plasminogen receptor with a C-terminal lysine
NDUFA12 NADH:ubiquinone oxidoreductase subunit A12
UBL5 ubiquitin like 5
MRPL40 mitochondrial ribosomal protein L40
CUEDC2 CUE domain containing 2
NAA38 N-alpha-acetyltransferase 38, NatC auxiliary subunit
ATP5MK ATP synthase membrane subunit k
COX14 cytochrome c oxidase assembly factor COX14
MRPS36 mitochondrial ribosomal protein S36
ATP5IF1 ATP synthase inhibitory factor subunit 1
PTPMT1 protein tyrosine phosphatase mitochondrial 1
MRPL54 mitochondrial ribosomal protein L54
CHCHD1 coiled-coil-helix-coiled-coil-helix domain containing 1
MICOS13 mitochondrial contact site and cristae organizing system subunit 13
TRAPPC5 trafficking protein particle complex subunit 5
NDUFA11 NADH:ubiquinone oxidoreductase subunit A11
HIGD2A HIG1 hypoxia inducible domain family member 2A
MTLN mitoregulin
MRPL21 mitochondrial ribosomal protein L21
NDUFS7 NADH:ubiquinone oxidoreductase core subunit S7
BOLA3 bolA family member 3
CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10
GTF2H5 general transcription factor IIH subunit 5
MICOS10 mitochondrial contact site and cristae organizing system subunit 10
OST4 oligosaccharyltransferase complex subunit 4, non-catalytic
PET100 PET100 cytochrome c oxidase chaperone
Symbol Function*
Aco2 aconitase 2, mitochondrial
Slc25a4 solute carrier family 25 (mitochondrial carrier, adenine nucleotide translocator), member 4
Slc25a5 solute carrier family 25 (mitochondrial carrier, adenine nucleotide translocator), member 5
Prdx3 peroxiredoxin 3
Atox1 antioxidant 1 copper chaperone
Atp4a ATPase, H+/K+ exchanging, gastric, alpha polypeptide
Atp5a1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1
Atp5b ATP synthase, H+ transporting mitochondrial F1 complex, beta subunit
Atp5c1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1
Atp5pb ATP synthase peripheral stalk-membrane subunit b
Atp5g1 ATP synthase, H+ transporting, mitochondrial F0 complex, subunit C1 (subunit 9)
Atp5j ATP synthase, H+ transporting, mitochondrial F0 complex, subunit F
Atp5k ATP synthase, H+ transporting, mitochondrial F1F0 complex, subunit E
Atp6v1a ATPase, H+ transporting, lysosomal V1 subunit A
Atp6v1b2 ATPase, H+ transporting, lysosomal V1 subunit B2
Atp6v0d1 ATPase, H+ transporting, lysosomal V0 subunit D1
Atp6v1e1 ATPase, H+ transporting, lysosomal V1 subunit E1
Atp6v0e ATPase, H+ transporting, lysosomal V0 subunit E
Atpif1 ATPase inhibitory factor 1
Atp6v0c ATPase, H+ transporting, lysosomal V0 subunit C
Coq7 demethyl-Q 7
Cox17 cytochrome c oxidase assembly protein 17, copper chaperone
Cox4i1 cytochrome c oxidase subunit 4I1
Cox5a cytochrome c oxidase subunit 5A
Cox5b cytochrome c oxidase subunit 5B
Cox6a1 cytochrome c oxidase subunit 6A1
Cox6a2 cytochrome c oxidase subunit 6A2
Cox6c cytochrome c oxidase subunit 6C
Cox7a1 cytochrome c oxidase subunit 7A1
Cox7a2 cytochrome c oxidase subunit 7A2
Cox7c cytochrome c oxidase subunit 7C
Cox8a cytochrome c oxidase subunit 8A
Cox8b cytochrome c oxidase subunit 8B
Cycs cytochrome c, somatic
Dbi diazepam binding inhibitor
Dld dihydrolipoamide dehydrogenase
Chchd2 coiled-coil-helix-coiled-coil-helix domain containing 2
Fh1 fumarate hydratase 1
Foxi1 forkhead box I1
Bloc1s1 biogenesis of lysosomal organelles complex-1, subunit 1
Mrps33 mitochondrial ribosomal protein S33
Got2 glutamatic-oxaloacetic transaminase 2, mitochondrial
Hint1 histidine triad nucleotide binding protein 1
Idh3g isocitrate dehydrogenase 3 (NAD+), gamma
Mb myoglobin
Mdh2 malate dehydrogenase 2, NAD (mitochondrial)
Mdh1 malate dehydrogenase 1, NAD (soluble)
Ndufa2 NADH:ubiquinone oxidoreductase subunit A2
Ndufa4 Ndufa4, mitochondrial complex associated
Ndufs4 NADH:ubiquinone oxidoreductase core subunit S4
Ndufv1 NADH:ubiquinone oxidoreductase core subunit V1
Nsf N-ethylmaleimide sensitive fusion protein
Pdha1 pyruvate dehydrogenase E1 alpha 1
Phb prohibitin
Slc25a3 solute carrier family 25 (mitochondrial carrier, phosphate carrier), member 3
Pex19 peroxisomal biogenesis factor 19
Rpl30 ribosomal protein L30
Sod1 superoxide dismutase 1, soluble
Sod2 superoxide dismutase 2, mitochondrial
Uqcrq ubiquinol-cytochrome c reductase, complex III subunit VII
Uqcrc1 ubiquinol-cytochrome c reductase core protein 1
Vdac2 voltage-dependent anion channel 2
Ecsit ECSIT signalling integrator
Atp5l ATP synthase, H+ transporting, mitochondrial F0 complex, subunit G
Gfm1 G elongation factor, mitochondrial 1
Atp5o ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit
Timm8b translocase of inner mitochondrial membrane 8B
Cisd1 CDGSH iron sulfur domain 1
Mtx2 metaxin 2
Ndufa1 NADH:ubiquinone oxidoreductase subunit A1
Atp6ap1 ATPase, H+ transporting, lysosomal accessory protein 1
Mpc1 mitochondrial pyruvate carrier 1
Mrpl37 mitochondrial ribosomal protein L37
Mtch2 mitochondrial carrier 2
Suclg1 succinate-CoA ligase, GDP-forming, alpha subunit
Park7 Parkinson disease (autosomal recessive, early onset) 7
Atp5j2 ATP synthase, H+ transporting, mitochondrial F0 complex, subunit F2
Atp5d ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit
Ndufb5 NADH:ubiquinone oxidoreductase subunit B5
Sdhc succinate dehydrogenase complex, subunit C, integral membrane protein
Aurkaip1 aurora kinase A interacting protein 1
Ndufa3 NADH:ubiquinone oxidoreductase subunit A3
Lamtor4 late endosomal/lysosomal adaptor, MAPK and MTOR activator 4
Ndufa9 NADH:ubiquinone oxidoreductase subunit A9
Fmc1 formation of mitochondrial complex V assembly factor 1
Mrps36 mitochondrial ribosomal protein S36
Cox7b cytochrome c oxidase subunit 7B
Atp6v1f ATPase, H+ transporting, lysosomal V1 subunit F
Dnajc15 DnaJ heat shock protein family (Hsp40) member C15
Uqcr10 ubiquinol-cytochrome c reductase, complex III subunit X
Mrpl4 mitochondrial ribosomal protein L4
Tomm7 translocase of outer mitochondrial membrane 7
Nop10 NOP10 ribonucleoprotein
Ndufb9 NADH:ubiquinone oxidoreductase subunit B9
Mrps16 mitochondrial ribosomal protein S16
Atp6v1g1 ATPase, H+ transporting, lysosomal V1 subunit G1
Mrps21 mitochondrial ribosomal protein S21
Atp6v1c1 ATPase, H+ transporting, lysosomal V1 subunit C1
Ndufc1 NADH:ubiquinone oxidoreductase subunit C1
Ndufa12 NADH:ubiquinone oxidoreductase subunit A12
Chchd7 coiled-coil-helix-coiled-coil-helix domain containing 7
Cyc1 cytochrome c-1
Atp5md ATP synthase membrane subunit DAPIT
Polr2l polymerase (RNA) II (DNA directed) polypeptide L
Mrpl51 mitochondrial ribosomal protein L51
Ndufb3 NADH:ubiquinone oxidoreductase subunit B3
Uqcrh ubiquinol-cytochrome c reductase hinge protein
Uqcr11 ubiquinol-cytochrome c reductase, complex III subunit XI
Uqcrfs1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
Emc2 ER membrane protein complex subunit 2
Acot13 acyl-CoA thioesterase 13
Pmpca peptidase (mitochondrial processing) alpha
Ndufb7 NADH:ubiquinone oxidoreductase subunit B7
Sdhd succinate dehydrogenase complex, subunit D, integral membrane protein
Sdha succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
Uqcrc2 ubiquinol cytochrome c reductase core protein 2
Higd2a HIG1 domain family, member 2A
Romo1 reactive oxygen species modulator 1
Atp5e ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit
Ndufa6 NADH:ubiquinone oxidoreductase subunit A6
Arl8b ADP-ribosylation factor-like 8B
Ndufa13 NADH:ubiquinone oxidoreductase subunit A13
Ndufb8 NADH:ubiquinone oxidoreductase subunit B8
Mrpl42 mitochondrial ribosomal protein L42
Ndufa10 NADH:ubiquinone oxidoreductase subunit A10
Uqcrb ubiquinol-cytochrome c reductase binding protein
Sdhb succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
Mtres1 mitochondrial transcription rescue factor 1
Slc25a11 solute carrier family 25 (mitochondrial carrier oxoglutarate carrier), member 11
Ppa1 pyrophosphatase (inorganic) 1
Trap1 TNF receptor-associated protein 1
Ndufb4 NADH:ubiquinone oxidoreductase subunit B4
Ndufc2 NADH:ubiquinone oxidoreductase subunit C2
Ndufb2 NADH:ubiquinone oxidoreductase subunit B2
Ndufa5 NADH:ubiquinone oxidoreductase subunit A5
Pdhb pyruvate dehydrogenase (lipoamide) beta
Ndufb10 NADH:ubiquinone oxidoreductase subunit B10
Ndufs3 NADH:ubiquinone oxidoreductase core subunit S3
Ndufa8 NADH:ubiquinone oxidoreductase subunit A8
Mrpl58 mitochondrial ribosomal protein L58
Mrpl28 mitochondrial ribosomal protein L28
Samm50 SAMM50 sorting and assembly machinery component
Atp6v1c2 ATPase, H+ transporting, lysosomal V1 subunit C2
Smdt1 single-pass membrane protein with aspartate rich tail 1
Fuom fucose mutarotase
Tmem256 transmembrane protein 256
2310061I04Rik RIKEN cDNA 2310061I04 gene
Cox11 cytochrome c oxidase assembly protein 11, copper chaperone
Tmem147 transmembrane protein 147
Ndufa11 NADH:ubiquinone oxidoreductase subunit A11
Atp5mpl ATP synthase membrane subunit 6.8PL
Ndufab1 NADH:ubiquinone oxidoreductase subunit AB1
Cox10 heme A:farnesyltransferase cytochrome c oxidase assembly factor 10
Mpc2 mitochondrial pyruvate carrier 2
Atp6ap2 ATPase, H+ transporting, lysosomal accessory protein 2
Atp5h ATP synthase, H+ transporting, mitochondrial F0 complex, subunit D
Ndufv2 NADH:ubiquinone oxidoreductase core subunit V2
Atp6v1d ATPase, H+ transporting, lysosomal V1 subunit D
Ppa2 pyrophosphatase (inorganic) 2
Ndufs7 NADH:ubiquinone oxidoreductase core subunit S7
Acyp2 acylphosphatase 2, muscle type
Higd1b HIG1 domain family, member 1B
Immt inner membrane protein, mitochondrial
Ckmt2 creatine kinase, mitochondrial 2
Tmem213 transmembrane protein 213
Naa38 N(alpha)-acetyltransferase 38, NatC auxiliary subunit
Ndufv3 NADH:ubiquinone oxidoreductase core subunit V3
Cox4i2 cytochrome c oxidase subunit 4I2
Ptges2 prostaglandin E synthase 2
D8Ertd738e DNA segment, Chr 8, ERATO Doi 738, expressed
Chchd10 coiled-coil-helix-coiled-coil-helix domain containing 10
Ndufb11 NADH:ubiquinone oxidoreductase subunit B11
AI413582 expressed sequence AI413582
Mrpl30 mitochondrial ribosomal protein L30
Napa N-ethylmaleimide sensitive fusion protein attachment protein alpha
Atp6v1h ATPase, H+ transporting, lysosomal V1 subunit H
Cox6b1 cytochrome c oxidase, subunit 6B1
Atp6v1b1 ATPase, H+ transporting, lysosomal V1 subunit B1
Atp6v0b ATPase, H+ transporting, lysosomal V0 subunit B
Bsnd barttin CLCNK type accessory beta subunit
Atp6v0a4 ATPase, H+ transporting, lysosomal V0 subunit A4
Idh3b isocitrate dehydrogenase 3 (NAD+) beta
Atp12a ATPase, H+/K+ transporting, nongastric, alpha polypeptide
Micos13 mitochondrial contact site and cristae organizing system subunit 13
Ndufs8 NADH:ubiquinone oxidoreductase core subunit S8
Cox15 cytochrome c oxidase assembly protein 15
Ndufs2 NADH:ubiquinone oxidoreductase core subunit S2
Ndufs1 NADH:ubiquinone oxidoreductase core subunit S1
Atp5g3 ATP synthase, H+ transporting, mitochondrial F0 complex, subunit C3 (subunit 9)
Ndufb6 NADH:ubiquinone oxidoreductase subunit B6
Tufm Tu translation elongation factor, mitochondrial
Nceh1 neutral cholesterol ester hydrolase 1
Atp6v1g3 ATPase, H+ transporting, lysosomal V1 subunit G3
Serf2 small EDRK-rich factor 2
Ndufs6 NADH:ubiquinone oxidoreductase core subunit S6
Ndufa4l2 Ndufa4, mitochondrial complex associated like 2
Micos10 mitochondrial contact site and cristae organizing system subunit 10
Ndufs5 NADH:ubiquinone oxidoreductase core subunit S5
Gpx4 glutathione peroxidase 4
Pet100 PET100 homolog
Ndufb1 NADH:ubiquinone oxidoreductase subunit B1
LOC118568718 NADH-ubiquinone oxidoreductase chain 5-like
Symbol Function*
Fh fumarate hydratase
Mdh1 malate dehydrogenase 1
Dbi diazepam binding inhibitor, acyl-CoA binding protein
Slc25a5 solute carrier family 25 member 5
Coq7 coenzyme Q7, hydroxylase
Cox8b cytochrome c oxidase, subunit VIIIb
Cox6a2 cytochrome c oxidase subunit 6A2
Cox6a1 cytochrome c oxidase subunit 6A1
Cstb cystatin B
Cycs cytochrome c, somatic
Ndufa5 NADH:ubiquinone oxidoreductase subunit A5
Got2 glutamic-oxaloacetic transaminase 2
Cox4i1 cytochrome c oxidase subunit 4i1
Pdha1 pyruvate dehydrogenase E1 subunit alpha 1
Atp5mc1 ATP synthase membrane subunit c locus 1
Timm17a translocase of inner mitochondrial membrane 17A
Cox6c cytochrome c oxidase subunit 6C
Mb myoglobin
Pmpcb peptidase, mitochondrial processing subunit beta
Slc25a11 solute carrier family 25 member 11
Prdx3 peroxiredoxin 3
Timm8b translocase of inner mitochondrial membrane 8 homolog B
Ndufv3 NADH:ubiquinone oxidoreductase subunit V3
Atp5f1a ATP synthase F1 subunit alpha
Txn2 thioredoxin 2
Ndufv2 NADH:ubiquinone oxidoreductase core subunit V2
Mdh2 malate dehydrogenase 2
Polr2f RNA polymerase II, I and III subunit F
Atp6ap1 ATPase H+ transporting accessory protein 1
Nme2 NME/NM23 nucleoside diphosphate kinase 2
Cox4i2 cytochrome c oxidase subunit 4i2
Cox17 cytochrome c oxidase copper chaperone COX17
Atp6v0e1 ATPase H+ transporting V0 subunit e1
Idh3b isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit beta
Cox5b cytochrome c oxidase subunit 5B
Prdx5 peroxiredoxin 5
Gfm1 G elongation factor, mitochondrial 1
Suclg1 succinate-CoA ligase GDP/ADP-forming subunit alpha
Atp5mc3 ATP synthase membrane subunit c locus 3
Atp5f1c ATP synthase F1 subunit gamma
Ap2m1 adaptor related protein complex 2 subunit mu 1
Atp6v1f ATPase H+ transporting V1 subunit F
Atp6v1b2 ATPase H+ transporting V1 subunit B2
Atp5me ATP synthase membrane subunit e
Sdha succinate dehydrogenase complex flavoprotein subunit A
Atp6v0c ATPase H+ transporting V0 subunit C
Atp5mk ATP synthase membrane subunit k
Atp5mc2 ATP synthase membrane subunit c locus 2
Mpc1 mitochondrial pyruvate carrier 1
Cox8a cytochrome c oxidase subunit 8A
Atp5f1b ATP synthase F1 subunit beta
Atp5pb ATP synthase peripheral stalk-membrane subunit b
Atp5po ATP synthase peripheral stalk subunit OSCP
Atp5f1e ATP synthase F1 subunit epsilon
Slc25a3 solute carrier family 25 member 3
Atp5f1d ATP synthase F1 subunit delta
Timm13 translocase of inner mitochondrial membrane 13
Cox5a cytochrome c oxidase subunit 5A
Foxi1 forkhead box I1
Tmem256 transmembrane protein 256
Rnasek ribonuclease K
Higd1b HIG1 hypoxia inducible domain family, member 1B
Ndufb4 NADH:ubiquinone oxidoreductase subunit B4
Mgst3 microsomal glutathione S-transferase 3
Sdhc succinate dehydrogenase complex subunit C
Ndufs2 NADH:ubiquinone oxidoreductase core subunit S2
Atp6v1g3 ATPase H+ transporting V1 subunit G3
Pdhb pyruvate dehydrogenase E1 subunit beta
Dnajc15 DnaJ heat shock protein family (Hsp40) member C15
Tmem255b transmembrane protein 255B
Prelid1 PRELI domain containing 1
Uqcrfs1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
Acot13 acyl-CoA thioesterase 13
Ndufa2 NADH:ubiquinone oxidoreductase subunit A2
Atp6v0d1 ATPase H+ transporting V0 subunit D1
Etfb electron transfer flavoprotein subunit beta
Ndufc2 NADH:ubiquinone oxidoreductase subunit C2
Mrpl48 mitochondrial ribosomal protein L48
Uqcrc2 ubiquinol cytochrome c reductase core protein 2
Ndufab1 NADH:ubiquinone oxidoreductase subunit AB1
Ndufs8 NADH:ubiquinone oxidoreductase core subunit S8
Ndufv1 NADH:ubiquinone oxidoreductase core subunit V1
mrpl11 mitochondrial ribosomal protein L11
Mrpl16 mitochondrial ribosomal protein L16
Mcee methylmalonyl CoA epimerase
Ndufb8 NADH:ubiquinone oxidoreductase subunit B8
Gatd3a glutamine amidotransferase class 1 domain containing 3A
Cisd1 CDGSH iron sulfur domain 1
Ppa1 inorganic pyrophosphatase 1
Mrps36 mitochondrial ribosomal protein S36
Ndufb5 NADH:ubiquinone oxidoreductase subunit B5
Tmx2 thioredoxin-related transmembrane protein 2
Ndufs3 NADH:ubiquinone oxidoreductase core subunit S3
Phpt1 phosphohistidine phosphatase 1
Ndufa8 NADH:ubiquinone oxidoreductase subunit A8
Atp6v0a4 ATPase H+ transporting V0 subunit a4
Bola3 bolA family member 3
Mrps25 mitochondrial ribosomal protein S25
Atp6v1e1 ATPase H+ transporting V1 subunit E1
Atp6v1h ATPase H+ transporting V1 subunit H
Mrpl15 mitochondrial ribosomal protein L15
Zbtb8os zinc finger and BTB domain containing 8 opposite strand
Ndufb6 NADH:ubiquinone oxidoreductase subunit B6
Atp6v1g1 ATPase H+ transporting V1 subunit G1
Atp6v0b ATPase H+ transporting V0 subunit B
Sdhb succinate dehydrogenase complex iron sulfur subunit B
Dld dihydrolipoamide dehydrogenase
Atp6v1d ATPase H+ transporting V1 subunit D
Dlst dihydrolipoamide S-succinyltransferase
Ndufb11 NADH:ubiquinone oxidoreductase subunit B11
Mrpl54 mitochondrial ribosomal protein L54
Ndufa7 NADH:ubiquinone oxidoreductase subunit A7
Ndufa12 NADH:ubiquinone oxidoreductase subunit A12
Mrpl42 mitochondrial ribosomal protein L42
Ndufb9 NADH:ubiquinone oxidoreductase subunit B9
Atp6v1c1 ATPase H+ transporting V1 subunit C1
Cyc1 cytochrome c-1
Samm50 SAMM50 sorting and assembly machinery component
Atp5mg ATP synthase membrane subunit g
Uqcrc1 ubiquinol-cytochrome c reductase core protein 1
Ndufa11 NADH:ubiquinone oxidoreductase subunit A11
Micos13 mitochondrial contact site and cristae organizing system subunit 13
Mrpl14 mitochondrial ribosomal protein L14
Ndufb3 NADH:ubiquinone oxidoreductase subunit B3
Ndufs1 NADH:ubiquinone oxidoreductase core subunit S1
Atp6ap2 ATPase H+ transporting accessory protein 2
Cox7b cytochrome c oxidase subunit 7B
Mrpl12 mitochondrial ribosomal protein L12
Cox15 cytochrome c oxidase assembly homolog COX15
Ptges2 prostaglandin E synthase 2
Immt inner membrane mitochondrial protein
Atp6v1b1 ATPase H+ transporting V1 subunit B1
Atpaf1 ATP synthase mitochondrial F1 complex assembly factor 1
Smdt1 single-pass membrane protein with aspartate-rich tail 1
Ndufa6 NADH:ubiquinone oxidoreductase subunit A6
Ndufa10l1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex 10-like 1
Cox8c cytochrome c oxidase subunit 8C
Fam162a family with sequence similarity 162, member A
Ndufb7 NADH:ubiquinone oxidoreductase subunit B7
Aamdc adipogenesis associated, Mth938 domain containing
Chchd10 coiled-coil-helix-coiled-coil-helix domain containing 10
Endog endonuclease G
Slc25a12 solute carrier family 25 member 12
Ndufb2 NADH:ubiquinone oxidoreductase subunit B2
Ndufa9 NADH:ubiquinone oxidoreductase subunit A9
Ndufs5 NADH:ubiquinone oxidoreductase subunit S5
Micos10 mitochondrial contact site and cristae organizing system subunit 10
Ndufs7 NADH:ubiquinone oxidoreductase core subunit S7
Uqcrb ubiquinol-cytochrome c reductase binding protein
Mrpl4 mitochondrial ribosomal protein L4
Sdhd succinate dehydrogenase complex subunit D
Ndufa1 NADH:ubiquinone oxidoreductase subunit A1
Apoo apolipoprotein O
Piwil1 piwi-like RNA-mediated gene silencing 1
Uqcrh ubiquinol-cytochrome c reductase hinge protein
Atp6v0e2 ATPase, H+ transporting V0 subunit e2
Ccdc7 coiled-coil domain containing 7
Uqcrq ubiquinol-cytochrome c reductase, complex III subunit VII
Coq9 coenzyme Q9
Ndufs4 NADH:ubiquinone oxidoreductase subunit S4
Fmc1 formation of mitochondrial complex V assembly factor 1
Ubl5 ubiquitin-like 5
Dnajc19 DnaJ heat shock protein family (Hsp40) member C19
Atp5pd ATP synthase peripheral stalk subunit d
Ndufa10 NADH:ubiquinone oxidoreductase subunit A10
Romo1 reactive oxygen species modulator 1
LOC679739 NADH dehydrogenase (ubiquinone) Fe-S protein 6
Pam16 presequence translocase associated motor 16
Ndufa4 NDUFA4, mitochondrial complex associated
Cox14 cytochrome c oxidase assembly factor COX14
Cops9 COP9 signalosome subunit 9
Ndufb10 NADH:ubiquinone oxidoreductase subunit B10
Atp6v1a ATPase H+ transporting V1 subunit A
Uqcr10 ubiquinol-cytochrome c reductase, complex III subunit X
Cox7a1 cytochrome c oxidase subunit 7A1
Cox6b1 cytochrome c oxidase subunit 6B1
Mrps16 mitochondrial ribosomal protein S16
Tmem213 transmembrane protein 213
Ndufc1 NADH:ubiquinone oxidoreductase subunit C1
Atp5mf ATP synthase membrane subunit f
Hint1 histidine triad nucleotide binding protein 1
Uqcr11 ubiquinol-cytochrome c reductase, complex III subunit XI
Ndufaf8 NADH:ubiquinone oxidoreductase complex assembly factor 8
Ndufa3 NADH:ubiquinone oxidoreductase subunit A3
Cox10 cytochrome c oxidase assembly factor heme A:farnesyltransferase COX10
Cox7c cytochrome c oxidase subunit 7C
Mpc2 mitochondrial pyruvate carrier 2
Cox7b2 cytochrome c oxidase subunit 7B2
Ndufa4l2 NDUFA4, mitochondrial complex associated like 2
Cmc2 C-x(9)-C motif containing 2
LOC100363502 cytochrome c, somatic-like
Ndufa13 NADH:ubiquinone oxidoreductase subunit A13
Ndufb1 NADH:ubiquinone oxidoreductase subunit B1
LOC100912557 6.8 kDa mitochondrial proteolipid-like
Coa6 cytochrome c oxidase assembly factor 6
LOC103693330 up-regulated during skeletal muscle growth protein 5 pseudogene
Cox11 cytochrome c oxidase copper chaperone COX11
Mtln mitoregulin
LOC120099911 ATP synthase subunit ATP5MPL, mitochondrial
LOC120102958 uncharacterized LOC120102958
Symbol Function*
ACO2 aconitase 2
NDUFS4 NADH:ubiquinone oxidoreductase subunit S4
ATP5F1AZ ATP synthase F1 subunit alpha Z chromosome
MRPL23 mitochondrial ribosomal protein L23
DBI diazepam binding inhibitor, acyl-CoA binding protein
PARK7 Parkinsonism associated deglycase
CHURC1 churchill domain containing 1
ATP6V1B2 ATPase H+ transporting V1 subunit B2
VDAC2 voltage dependent anion channel 2
SDHA succinate dehydrogenase complex flavoprotein subunit A
ATP6V1A ATPase H+ transporting V1 subunit A
GOT2 glutamic-oxaloacetic transaminase 2
NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa
ETFA electron transfer flavoprotein alpha subunit
IDH3A isocitrate dehydrogenase 3 (NAD(+)) alpha
COQ9 coenzyme Q9
ATP6V0D1 ATPase H+ transporting V0 subunit d1
UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
GCSH glycine cleavage system protein H
COX4I1 cytochrome c oxidase subunit 4I1
SMIM4 small integral membrane protein 4
UQCRC1 ubiquinol-cytochrome c reductase core protein 1
PDHB pyruvate dehydrogenase (lipoamide) beta
UQCRQ ubiquinol-cytochrome c reductase complex III subunit VII
NDFIP1 Nedd4 family interacting protein 1
NDUFB6 NADH:ubiquinone oxidoreductase subunit B6
ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex subunit F2
NDUFB10 NADH:ubiquinone oxidoreductase subunit B10
NDUFAB1 NADH:ubiquinone oxidoreductase subunit AB1
COQ7 coenzyme Q7, hydroxylase
ECI1 enoyl-CoA delta isomerase 1
PAM16 presequence translocase associated motor 16 homolog
ATP6V0C ATPase H+ transporting V0 subunit c
CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10
COX6A1 cytochrome c oxidase subunit 6A1
MTFP1 mitochondrial fission process 1
NDUFA8 NADH:ubiquinone oxidoreductase subunit A8
ATP6V1G1 ATPase H+ transporting V1 subunit G1
TMEM141 transmembrane protein 141
COX10 COX10, heme A:farnesyltransferase cytochrome c oxidase assembly factor
MDH2 malate dehydrogenase 2
NIPSNAP2 nipsnap homolog 2
CHCHD2P9 coiled-coil-helix-coiled-coil-helix domain containing 2 pseudogene 9
CLUH clustered mitochondria homolog
DLD dihydrolipoamide dehydrogenase
NDUFA5 NADH:ubiquinone oxidoreductase subunit A5
NDUFA12 NADH:ubiquinone oxidoreductase subunit A12
SLC25A3 solute carrier family 25 member 3
ATP6V0A4 ATPase H+ transporting V0 subunit a4
NDUFB2 NADH:ubiquinone oxidoreductase subunit B2
ATP6V1E1 ATPase H+ transporting V1 subunit E1
SAMM50 SAMM50 sorting and assembly machinery component
FAM162A family with sequence similarity 162 member A
ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex subunit F6
ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit
NDUFV3 NADH:ubiquinone oxidoreductase subunit V3
ATP6AP2 ATPase H+ transporting accessory protein 2
APOO apolipoprotein O
PDHA2 pyruvate dehydrogenase (lipoamide) alpha 2
NDUFA9 NADH:ubiquinone oxidoreductase subunit A9
ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1
ACOT7 acyl-CoA thioesterase 7
MINOS1 mitochondrial inner membrane organizing system 1
NFYC nuclear transcription factor Y subunit gamma
SDHD succinate dehydrogenase complex subunit D
ATP5PB ATP synthase peripheral stalk-membrane subunit b
TOMM6 translocase of outer mitochondrial membrane 6
PHB prohibitin
ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex subunit C1 (subunit 9)
NDUFA7 NADH:ubiquinone oxidoreductase subunit A7
ATP6V0D2 ATPase H+ transporting V0 subunit d2
UQCRB ubiquinol-cytochrome c reductase binding protein
COX6C cytochrome c oxidase subunit 6C
ATP6V1C1 ATPase H+ transporting V1 subunit C1
HADH hydroxyacyl-CoA dehydrogenase
NDUFB9 NADH:ubiquinone oxidoreductase subunit B9
TBRG4 transforming growth factor beta regulator 4
CYCS cytochrome c, somatic
LOC420860 transmembrane protein 14C-like
NDUFS6 NADH:ubiquinone oxidoreductase subunit S6
TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast)
MDH1 malate dehydrogenase 1
COX7A2L cytochrome c oxidase subunit 7A2 like
ATP6V1C2 ATPase H+ transporting V1 subunit C2
ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex subunit D
OCIAD2 OCIA domain containing 2
IMMT inner membrane mitochondrial protein
SUCLG1 succinate-CoA ligase alpha subunit
TMEM258 transmembrane protein 258
NDUFS3 NADH:ubiquinone oxidoreductase core subunit S3
ATP6V1D ATPase H+ transporting V1 subunit D
DLST dihydrolipoamide S-succinyltransferase
NDUFB1 NADH:ubiquinone oxidoreductase subunit B1
GHITM growth hormone inducible transmembrane protein
NDUFB8 NADH:ubiquinone oxidoreductase subunit B8
USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse)
NDUFA10 NADH:ubiquinone oxidoreductase subunit A10
NDUFB3 NADH:ubiquinone oxidoreductase subunit B3
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex subunit C3 (subunit 9)
METAP1D methionyl aminopeptidase type 1D, mitochondrial
NAA20 N(alpha)-acetyltransferase 20, NatB catalytic subunit
ATP6V1G3 ATPase H+ transporting V1 subunit G3
MRPS14 mitochondrial ribosomal protein S14
ATP6V0B ATPase H+ transporting V0 subunit b
NDUFB5 NADH:ubiquinone oxidoreductase subunit B5
ATP6V1H ATPase H+ transporting V1 subunit H
NDUFV2 NADH:ubiquinone oxidoreductase core subunit V2
IDH3B isocitrate dehydrogenase 3 (NAD(+)) beta
ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide
MRPL34 mitochondrial ribosomal protein L34
TXN2 thioredoxin 2
UQCRC2 ubiquinol-cytochrome c reductase core protein II
NDUFA6 NADH:ubiquinone oxidoreductase subunit A6
AIFM1 apoptosis inducing factor, mitochondria associated 1
PRDX3 peroxiredoxin 3
NDUFV1 NADH:ubiquinone oxidoreductase core subunit V1
IDH2 isocitrate dehydrogenase (NADP(+)) 2, mitochondrial
COX7C cytochrome c oxidase subunit 7C
CAPN1 calpain 1
ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit
NDUFA2 NADH:ubiquinone oxidoreductase subunit A2
HSCB HscB mitochondrial iron-sulfur cluster cochaperone
MRPL12 mitochondrial ribosomal protein L12
ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex subunit E
PPA1 inorganic pyrophosphatase 1
NDUFS8 NADH:ubiquinone oxidoreductase core subunit S8
COX5A cytochrome c oxidase subunit 5A
PFKL phosphofructokinase, liver type
NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa
UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI
COX17 COX17, cytochrome c oxidase copper chaperone
MYCBP MYC binding protein
POLR2L RNA polymerase II subunit L
NDUFS7 NADH:ubiquinone oxidoreductase core subunit S7
SMDT1 single-pass membrane protein with aspartate rich tail 1
UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X
MRPS36 mitochondrial ribosomal protein S36
IMMP1L inner mitochondrial membrane peptidase subunit 1
ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit
NDUFS5 NADH:ubiquinone oxidoreductase subunit S5
UQCRHL ubiquinol-cytochrome c reductase hinge protein like
COX7B cytochrome c oxidase subunit 7B
NDUFA4 NDUFA4, mitochondrial complex associated
NDUFA1 NADH:ubiquinone oxidoreductase subunit A1
C14orf2 chromosome 14 open reading frame 2
COX7A2 cytochrome c oxidase subunit 7A2
COX8A cytochrome c oxidase subunit 8A
NDUFS2 NADH:ubiquinone oxidoreductase core subunit S2
ATPIF1 ATPase inhibitory factor 1
C19orf70 chromosome 19 open reading frame 70
ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex subunit C2 (subunit 9)
DMRT2 doublesex and mab-3 related transcription factor 2
NDUFA13 NADH:ubiquinone oxidoreductase subunit A13
PFDN5 prefoldin subunit 5
SDHC succinate dehydrogenase complex subunit C
SDHB succinate dehydrogenase complex iron sulfur subunit B
ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex subunit G
LYRM9 LYR motif containing 9
LOC107049545 cytochrome c oxidase subunit 5B, mitochondrial
LOC107050595 basic proline-rich protein-like
LOC107052326 uncharacterized LOC107052326
MRPL36 mitochondrial ribosomal protein L36
BSND Bartter syndrome, infantile, with sensorineural deafness (Barttin)
LOC107055082 cytochrome b5 domain-containing protein 1-like
LOC121106727 uncharacterized LOC121106727
LOC121108888 cytochrome c oxidase subunit 6B1
NDUFB11 NADH:ubiquinone oxidoreductase subunit B11
Symbol Function*
nipsnap2 nipsnap homolog 2
mtch2 mitochondrial carrier homolog 2
alas1 aminolevulinate, delta-, synthase 1
hsd17b8 hydroxysteroid (17-beta) dehydrogenase 8
atp5mc3b ATP synthase membrane subunit c locus 3b
atp6v1e1b ATPase H+ transporting V1 subunit E1b
atp6v0ca ATPase H+ transporting V0 subunit ca
atp6ap1b ATPase H+ transporting accessory protein 1b
mtx2 metaxin 2
atp6v1h ATPase H+ transporting V1 subunit H
tomm22 translocase of outer mitochondrial membrane 22 homolog (yeast)
mpc2b mitochondrial pyruvate carrier 2b
atp6v0b ATPase H+ transporting V0 subunit b
ndufa10 NADH:ubiquinone oxidoreductase subunit A10
cs citrate synthase
slc25a3b solute carrier family 25 member 3b
uqcrc2b ubiquinol-cytochrome c reductase core protein 2b
aco2 aconitase 2, mitochondrial
atp6v0d1 ATPase H+ transporting V0 subunit d1
ankhb ANKH inorganic pyrophosphate transport regulator b
atp6v0a1a ATPase H+ transporting V0 subunit a1a
atp6v0cb ATPase H+ transporting V0 subunit cb
ndufab1b NADH:ubiquinone oxidoreductase subunit AB1b
cox5ab cytochrome c oxidase subunit 5Ab
cox4i1 cytochrome c oxidase subunit 4I1
atp5l ATP synthase, H+ transporting, mitochondrial F0 complex, subunit g
adsl adenylosuccinate lyase
wdr13 WD repeat domain 13
atp6v1g1 ATPase H+ transporting V1 subunit G1
atp5po ATP synthase peripheral stalk subunit OSCP
atp5f1d ATP synthase F1 subunit delta
cox7a2l cytochrome c oxidase subunit 7A2 like
cox6a1 cytochrome c oxidase subunit 6A1
got2b glutamic-oxaloacetic transaminase 2b, mitochondrial
cox7c cytochrome c oxidase subunit 7C
rnasekb ribonuclease, RNase K b
fam162a family with sequence similarity 162 member A
atp5f1c ATP synthase F1 subunit gamma
atp6v1ab ATPase H+ transporting V1 subunit Ab
slc25a12 solute carrier family 25 member 12
gpx4b glutathione peroxidase 4b
atp6v1ba ATPase, H+ transporting, lysosomal, V1 subunit B, member a
atp6v1b2 ATPase H+ transporting V1 subunit B2
dlst dihydrolipoamide S-succinyltransferase
atp6v1c1a ATPase H+ transporting V1 subunit C1a
prdx3 peroxiredoxin 3
aifm1 apoptosis inducing factor mitochondrion associated 1
idh2 isocitrate dehydrogenase (NADP(+)) 2
samm50 SAMM50 sorting and assembly machinery component
cox6b2 cytochrome c oxidase subunit 6B2
ndufa11 NADH:ubiquinone oxidoreductase subunit A11
atp5pd ATP synthase peripheral stalk subunit d
ndufa13 NADH:ubiquinone oxidoreductase subunit A13
ndufa8 NADH:ubiquinone oxidoreductase subunit A8
ndufb10 NADH:ubiquinone oxidoreductase subunit B10
ndufv2 NADH:ubiquinone oxidoreductase core subunit V2
dnajc19 DnaJ (Hsp40) homolog, subfamily C, member 19
chchd2 coiled-coil-helix-coiled-coil-helix domain containing 2
chchd10 coiled-coil-helix-coiled-coil-helix domain containing 10
ndufb2 NADH:ubiquinone oxidoreductase subunit B2
pam16 presequence translocase associated motor 16
ndufb6 NADH:ubiquinone oxidoreductase subunit B
uqcrc1 ubiquinol-cytochrome c reductase core protein 1
cops9 COP9 signalosome subunit 9
ndufb7 NADH:ubiquinone oxidoreductase subunit B7
ndufb8 NADH:ubiquinone oxidoreductase subunit B8
sdha succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
idh3a isocitrate dehydrogenase (NAD(+)) 3 catalytic subunit alpha
atp6v1d ATPase H+ transporting V1 subunit D
fh fumarate hydratase
ndufa6 NADH:ubiquinone oxidoreductase subunit A6
atp6v1aa ATPase H+ transporting V1 subunit Aa
hibadhb 3-hydroxyisobutyrate dehydrogenase b
atp5mc3a ATP synthase membrane subunit c locus 3a
dldh dihydrolipoamide dehydrogenase
cox4i1l cytochrome c oxidase subunit 4I1, like
atp5mf ATP synthase membrane subunit f
mmadhcb metabolism of cobalamin associated Db
txn2 thioredoxin 2
pccb propionyl-CoA carboxylase subunit beta
glrx5 glutaredoxin 5 homolog (S. cerevisiae)
atp6ap2 ATPase H+ transporting accessory protein 2
ndufa4b NDUFA4 mitochondrial complex associated b
sucla2 succinate-CoA ligase ADP-forming subunit beta
atp5mc1 ATP synthase membrane subunit c locus 1
ndufb4 NADH:ubiquinone oxidoreductase subunit B4
uqcrfs1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
mdh2 malate dehydrogenase 2, NAD (mitochondrial)
ndufs8a NADH:ubiquinone oxidoreductase core subunit S8a
pdhb pyruvate dehydrogenase E1 subunit beta
atp5pf ATP synthase peripheral stalk subunit F6
ndufa4a NDUFA4 mitochondrial complex associated a
cycsb cytochrome c, somatic b
ndufa1 NADH:ubiquinone oxidoreductase subunit A1
ap3m2 adaptor related protein complex 3 subunit mu 2
idh3b isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit beta
cox5ba cytochrome c oxidase subunit 5Ba
zgc:91860 zgc:91860
mpc1 mitochondrial pyruvate carrier 1
napgb N-ethylmaleimide-sensitive factor attachment protein, gamma b
sdhda succinate dehydrogenase complex, subunit D, integral membrane protein a
uqcrq ubiquinol-cytochrome c reductase, complex III subunit VII
atp6v1f ATPase H+ transporting V1 subunit F
ap3s2 adaptor related protein complex 3 subunit sigma 2
mrpl11 mitochondrial ribosomal protein L11
suclg1 succinate-CoA ligase GDP/ADP-forming subunit alph
sirt5 sirtuin 5
coq3 coenzyme Q3 methyltransferase
uqcrc2a ubiquinol-cytochrome c reductase core protein 2a
cox6b1 cytochrome c oxidase subunit 6B1
cox20 cytochrome c oxidase assembly factor COX20
trappc1 trafficking protein particle complex subunit 1
oxct1a 3-oxoacid CoA transferase 1a
ndufa7 NADH:ubiquinone oxidoreductase subunit A7
ndufa3 NADH:ubiquinone oxidoreductase subunit A3
sdhc succinate dehydrogenase complex, subunit C, integral membrane protein
ndufv1 NADH:ubiquinone oxidoreductase core subunit V1
sdhdb succinate dehydrogenase complex, subunit D, integral membrane protein b
ndufs6 NADH:ubiquinone oxidoreductase subunit S6
cox17 cytochrome c oxidase copper chaperone COX17
cox6a2 cytochrome c oxidase subunit 6A2
atp6v1c1b ATPase H+ transporting V1 subunit C1b
atp5pb ATP synthase peripheral stalk-membrane subunit b
atp6v0e1 ATPase H+ transporting V0 subunit e1
hsd17b10 hydroxysteroid (17-beta) dehydrogenase 10
chchd6b coiled-coil-helix-coiled-coil-helix domain containing 6b
mrpl16 mitochondrial ribosomal protein L16
ndufs1 NADH:ubiquinone oxidoreductase core subunit S1
cox6c cytochrome c oxidase subunit 6C
tomm5 translocase of outer mitochondrial membrane 5 homolog (yeast)
ndufaf1 NADH:ubiquinone oxidoreductase complex assembly factor 1
fxyd3 FXYD domain containing ion transport regulator 3
ndufa5 NADH:ubiquinone oxidoreductase subunit A5
ndufa9a NADH:ubiquinone oxidoreductase subunit A9a
ndufc2 NADH:ubiquinone oxidoreductase subunit C2
higd2a HIG1 hypoxia inducible domain family, member 2A
ndufs3 NADH:ubiquinone oxidoreductase core subunit S3
arhgap1 Rho GTPase activating protein 1
ndufs5 NADH:ubiquinone oxidoreductase subunit S5
ndufs2 NADH:ubiquinone oxidoreductase core subunit S2
mrps24 mitochondrial ribosomal protein S24
atp5fa1 ATP synthase F1 subunit alpha
fahd1 fumarylacetoacetate hydrolase domain containing 1
atpv0e2 ATPase H+ transporting V0 subunit e2
cox5aa cytochrome c oxidase subunit 5Aa
cox7a2a cytochrome c oxidase subunit 7A2a
ndufa2 NADH:ubiquinone oxidoreductase subunit A2
atp5f1b ATP synthase F1 subunit beta
uqcrb ubiquinol-cytochrome c reductase binding protein
ndufa12 NADH:ubiquinone oxidoreductase subunit A12
atp5mj ATP synthase membrane subunit j
cox8a cytochrome c oxidase subunit 8A
atp5if1b ATP synthase inhibitory factor subunit 1b
zgc:193742 zgc:193742
si:dkey-88p24.11 si:dkey-88p24.11
atp5mea ATP synthase membrane subunit ea
sdhb succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
ndufb11 NADH:ubiquinone oxidoreductase subunit B11
cox7b cytochrome c oxidase subunit 7B
acot13 acyl-CoA thioesterase 13
cyc1 cytochrome c-1
uqcrh ubiquinol-cytochrome c reductase hinge protein
mrps36 mitochondrial ribosomal protein S36
cox14 cytochrome c oxidase assembly factor COX14
afg3l2 AFG3-like AAA ATPase 2
mtbl metallothionein-B-like
cox8b cytochrome c oxidase subunit 8B
bckdhb branched chain keto acid dehydrogenase E1 subunit beta
zgc:162944 zgc:162944
ndufb9 NADH:ubiquinone oxidoreductase subunit B9
ndufab1a NADH:ubiquinone oxidoreductase subunit AB1a
ndufs4 NADH:ubiquinone oxidoreductase subunit S4
apooa apolipoprotein O, a
cox5b2 cytochrome c oxidase subunit 5B2
rnaseka ribonuclease, RNase K a
micos10 mitochondrial contact site and cristae organizing system subunit 10
tmem14ca transmembrane protein 14Ca
sdr39u1 short chain dehydrogenase/reductase family 39U, member 1
cox7a1 cytochrome c oxidase subunit 7A1
atp5meb ATP synthase membrane subunit eb
uqcc1 ubiquinol-cytochrome c reductase complex assembly factor 1
mrps12 mitochondrial ribosomal protein S12
atp5md ATP synthase membrane subunit k
mrps34 mitochondrial ribosomal protein S34
ndufs7 NADH:ubiquinone oxidoreductase core subunit S7
ndufb5 NADH:ubiquinone oxidoreductase subunit B5
atp5f1e ATP synthase F1 subunit epsilon
smdt1b single-pass membrane protein with aspartate-rich tail 1b
ndufc1 NADH:ubiquinone oxidoreductase subunit C1
mgarpa mitochondria localized glutamic acid rich protein a
ndufa4l2a NDUFA4 mitochondrial complex associated like 2a
atp6ap1a ATPase H+ transporting accessory protein 1a
zgc:194246 zgc:194246
atp5if1a ATP synthase inhibitory factor subunit 1a
coa3a cytochrome C oxidase assembly factor 3a
coa6 cytochrome c oxidase assembly factor 6
si:ch211-68a17.7 si:ch211-68a17.7
smim20 small integral membrane protein 20
si:ch1073-314i13.4 si:ch1073-314i13.4
si:dkey-85n7.8 si:dkey-85n7.8
LOC100331743 NAD(P) transhydrogenase, mitochondrial
ndufb3 NADH:ubiquinone oxidoreductase subunit B3
uqcr10 ubiquinol-cytochrome c reductase, complex III subunit X
si:ch1073-325m22.2 si:ch1073-325m22.2
ost4 oligosaccharyltransferase complex subunit 4 (non-catalytic)
pigbos1 PIGB opposite strand 1
cox7a2b cytochrome c oxidase subunit 7A2b
LOC100535417 fumarate hydratase, mitochondrial-like
LOC100535765 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 1
si:dkey-16p21.8 si:dkey-16p21.8
LOC100537077 uncharacterized LOC100537077
ndufv3 NADH:ubiquinone oxidoreductase subunit V3
atp6v1e1a ATPase H+ transporting V1 subunit E1a
Symbol Function*
CG14818 uncharacterized protein
ND-B14.5A NADH dehydrogenase (ubiquinone) B14.5 A subunit
VhaAC39-1 Vacuolar H[+] ATPase AC39 subunit 1
ND-B16.6 NADH dehydrogenase (ubiquinone) B16.6 subunit
ND-ASHI NADH dehydrogenase (ubiquinone) ASHI subunit
ND-75 NADH dehydrogenase (ubiquinone) 75 kDa subunit
ATPsyndelta ATP synthase, delta subunit
sesB stress-sensitive B
CG11752 uncharacterized protein
CG15719 uncharacterized protein
CG14407 uncharacterized protein
ND-B18 NADH dehydrogenase (ubiquinone) B18 subunit
CG9065 uncharacterized protein
CG8206 uncharacterized protein
ND-20 NADH dehydrogenase (ubiquinone) 20 kDa subunit
UQCR-14 Ubiquinol-cytochrome c reductase 14 kDa subunit
ND-24 NADH dehydrogenase (ubiquinone) 24 kDa subunit
Ucp4A Ucp4A
ND-18 NADH dehydrogenase (ubiquinone) 18 kDa subunit
Idh3a Isocitrate dehydrogenase 3a
COX6B Cytochrome c oxidase subunit 6B
ND-15 NADH dehydrogenase (ubiquinone) 15 kDa subunit
CG4270 uncharacterized protein
ND-B17.2 NADH dehydrogenase (ubiquinone) B17.2 subunit
ND-B14.5B NADH dehydrogenase (ubiquinone) B14.5 B subunit
mRpL28 mitochondrial ribosomal protein L28
ND-13A NADH dehydrogenase (ubiquinone) 13 kDa A subunit
ND-51 NADH dehydrogenase (ubiquinone) 51 kDa subunit
COX5B Cytochrome c oxidase subunit 5B
CG5037 uncharacterized protein
porin porin
CG16964 uncharacterized protein
ND-B22 NADH dehydrogenase (ubiquinone) B22 subunit
p38b p38b MAP kinase
ND-B17 NADH dehydrogenase (ubiquinone) B17 subunit
cni cornichon
Cyt-c-p Cytochrome c proximal
VhaSFD Vacuolar H[+]-ATPase SFD subunit
Jwa Jwa
COX4 Cytochrome c oxidase subunit 4
SdhB Succinate dehydrogenase, subunit B (iron-sulfur)
VhaAC45 Vacuolar H[+] ATPase AC45 accessory subunit
CG1814 uncharacterized protein
ND-B14 NADH dehydrogenase (ubiquinone) B14 subunit
Vha36-2 Vacuolar H[+] ATPase 36kD subunit 2
CG8818 uncharacterized protein
CG8768 uncharacterized protein
PheRS-m Phenylalanyl-tRNA synthetase, mitochondrial
ND-B15 NADH dehydrogenase (ubiquinone) B15 subunit
Vha14-1 Vacuolar H[+] ATPase 14kD subunit 1
Vha44 Vacuolar H[+] ATPase 44kD subunit
Sod2 Superoxide dismutase 2 (Mn)
UQCR-6.4 Ubiquinol-cytochrome c reductase 6.4 kDa subunit
CG14483 uncharacterized protein
SdhA Succinate dehydrogenase, subunit A (flavoprotein)
ND-B14.7 NADH dehydrogenase (ubiquinone) B14.7 subunit
ND-B12 NADH dehydrogenase (ubiquinone) B12 subunit
blw bellwether
levy levy
Nurf-38 Nucleosome remodeling factor - 38kD
ATPsynF ATP synthase, subunit F
ND-19 NADH dehydrogenase (ubiquinone) 19 kDa subunit
Tina-1 Troponin C-akin-1
ND-ACP NADH dehydrogenase (ubiquinone) acyl carrier protein
CG12091 uncharacterized protein
CG8993 uncharacterized protein
ND-30 NADH dehydrogenase (ubiquinone) 30 kDa subunit
Scsalpha1 Succinyl-coenzyme A synthetase alpha subunit 1
VhaM9.7-c Vacuolar H[+] ATPase M9.7 subunit c
Cyt-c1 Cytochrome c1
ATPsynB ATP synthase, subunit B
ND-13B NADH dehydrogenase (ubiquinone) 13 kDa B subunit
CG7551 uncharacterized protein
UQCR-C2 Ubiquinol-cytochrome c reductase core protein 2
QIL1 QIL1
UQCR-Q Ubiquinol-cytochrome c reductase ubiquinone-binding protein
CG7430 uncharacterized protein
CG14077 uncharacterized protein
ND-39 NADH dehydrogenase (ubiquinone) 39 kDa subunit
VhaM9.7-b Vacuolar H[+] ATPase M9.7 subunit b
COX8 Cytochrome c oxidase subunit 8
ND-B14.5AL NADH dehydrogenase (ubiquinone) B14.5 A subunit-like
Vha26 Vacuolar H[+]-ATPase 26kD subunit
elm ethanol sensitive with low memory
ATP6AP2 ATPase H+ transporting accessory protein 2
CG9399 uncharacterized protein
CG6629 uncharacterized protein
SdhC Succinate dehydrogenase, subunit C
CG5214 uncharacterized protein
COX5A Cytochrome c oxidase subunit 5A
GC1 Glutamate Carrier 1
Vha55 Vacuolar H[+]-ATPase 55kD subunit
ATPsynE ATP synthase, subunit E
UQCR-C1 Ubiquinol-cytochrome c reductase core protein 1
ATPsynO ATP synthase, oligomycin sensitivity conferring protein
l(3)neo43 lethal (3) neo43
CG5903 uncharacterized protein
CG10340 uncharacterized protein
Mdh2 Malate dehydrogenase 2
Vha100-2 Vacuolar H[+] ATPase 100kD subunit 2
NP15.6 NP15.6
ATPsynD ATP synthase, subunit D
Vha13 Vacuolar H[+] ATPase 13kD subunit
Idh3b Isocitrate dehydrogenase 3b
Mitofilin mitofilin
ND-42 NADH dehydrogenase (ubiquinone) 42 kDa subunit
ATPsynCF6 ATP synthase, coupling factor 6
SdhD Succinate dehydrogenase, subunit D
CG31098 uncharacterized protein
ND-49L NADH dehydrogenase (ubiquinone) 49 kDa subunit-like
CG6036 uncharacterized protein
UQCR-14L Ubiquinol-cytochrome c reductase 14 kDa subunit-like
Cisd2 CDGSH iron sulfur domain 2
ATPsyngamma ATP synthase, gamma subunit
Chchd3 Coiled-coil-helix-coiled-coil-helix domain containing 3
ATPsynC ATP synthase, subunit C
ND-49 NADH dehydrogenase (ubiquinone) 49 kDa subunit
ATPsynbeta ATP synthase, beta subunit
sun stunted
mAcon1 Mitochondrial aconitase 1
ND-23 NADH dehydrogenase (ubiquinone) 23 kDa subunit
ND-PDSW NADH dehydrogenase (ubiquinone) PDSW subunit
Vha16-1 Vacuolar H[+] ATPase 16kD subunit 1
RFeSP Rieske iron-sulfur protein
Vha36-1 Vacuolar H[+] ATPase 36kD subunit 1
CG3719 uncharacterized protein
Vha68-2 Vacuolar H[+] ATPase 68 kDa subunit 2
VhaPPA1-1 Vacuolar H[+] ATPase PPA1 subunit 1
ox oxen
cype cyclope
ATPsynG ATP synthase, subunit G
ND-SGDH NADH dehydrogenase (ubiquinone) SGDH subunit
dmGlut Dietary and metabolic glutamate transporter
Gpo1 Glycerophosphate oxidase 1
COX7A Cytochrome c oxidase subunit 7A
COX7C Cytochrome c oxidase subunit 7C
CG7630 uncharacterized protein
CG9034 uncharacterized protein
Neb-cGP Neb-cGP
CG18815 uncharacterized protein
Vha100-3 Vacuolar H[+] ATPase 100kD subunit 3
roh reduction of Rh1
ND-MLRQ NADH dehydrogenase (ubiquinone) MLRQ subunit
CG34148 uncharacterized protein
CG33170 uncharacterized protein
CG17691 uncharacterized protein
CG41128 uncharacterized protein
ND-AGGG NADH dehydrogenase (ubiquinone) AGGG subunit
UQCR-11 Ubiquinol-cytochrome c reductase 11 kDa subunit
CG34242 uncharacterized protein
ND-MWFE NADH dehydrogenase (ubiquinone) MWFE subunit
CG42376 uncharacterized protein
CG40472 uncharacterized protein
CG43329 uncharacterized protein
CG44242 uncharacterized protein
Symbol Function*
lpd-5 NADH dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrial
acbp-1 Acyl-CoA-binding protein homolog 1
got-2.1 Aspartate aminotransferase
rpl-41.1 60S ribosomal protein L41
F28B3.10 Uncharacterized protein
vha-16 V-type proton ATPase subunit
erm-1 Moesin/ezrin/radixin homolog 1
atp-3 ATP synthase subunit O, mitochondrial
vha-10 putative V-type proton ATPase subunit G
nuo-2 Complex I-30kD
gpc-2 G protein gamma domain-containing protein
nuo-6 Complex I-B15
D2030.4 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 7
cyc-1 Cytochrome c domain-containing protein
idha-1 putative isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial
asg-1 putative ATP synthase subunit g 1, mitochondrial
nduf-7 putative NADH dehydrogenase [ubiquinone] iron-sulfur protein 7, mitochondrial
cox-5B Cytochrome OXidase assembly protein
F59C6.5 NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 10
sdha-2 Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial
C34B2.8 Complex I-B16.6
atp-1 ATP synthase subunit alpha, mitochondrial
cox-4 Cytochrome OXidase assembly protein
Y63D3A.7 Complex I-B8
T02H6.11 Cytochrome b-c1 complex subunit 7
C25H3.9 Complex I-SGDH
F58F12.1 ATP synthase subunit delta, mitochondrial
vha-4 Vacuolar H ATPase
C18E9.4 Complex I-B12
F44G4.2 putative NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 2, mitochondrial
sdhb-1 Succinate dehydrogenase [ubiquinone] iron-sulfur subunit, mitochondrial
chch-3 MICOS complex subunit MIC19
R53.4 Putative ATP synthase subunit f, mitochondrial
vha-9 putative V-type proton ATPase subunit F
sdhd-1 Putative succinate dehydrogenase [ubiquinone] cytochrome b small subunit, mitochondrial
nuo-1 NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial
nduf-11 NADH Ubiquinone oxidoreductase Fe-S protein
vha-6 V-type proton ATPase subunit a
F44E5.1 Uncharacterized protein
Y38E10A.24 Uncharacterized protein
F32A11.1 Uncharacterized protein
F45H10.2 Complex III subunit 8
F45H10.3 Complex I-B14.5a
Y51H1A.3 Uncharacterized protein
cox-17 Cytochrome OXidase assembly protein
moma-1 MICOS complex subunit MIC27
ucr-2.3 Peptidase_M16 domain-containing protein
F23H11.5 Deltameth_res domain-containing protein
Y82E9BR.3 ATP synthase lipid-binding protein, mitochondrial
cisd-3.2 CDGSH Iron Sulfur Domain protein homolog
ddp-1 Mitochondrial import inner membrane translocase subunit Tim8
Y54F10AM.5 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8
Y71H2AM.4 Uncharacterized protein
nduf-9 NmrA domain-containing protein
prdx-3 putative peroxiredoxin prdx-3
idhg-1 Isocitrate dehydrogenase [NAD] subunit, mitochondrial
asb-1 ATP Synthase B homolog
cox-6A Cytochrome c oxidase subunit 6A, mitochondrial
atp-2 ATP synthase subunit beta, mitochondrial
ucr-1 Cytochrome b-c1 complex subunit 1, mitochondrial;Peptidase_M16_C domain-containing protein
C16A3.5 Complex I-B22
nuo-4 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrial;dNK domain-containing protein
F37C12.3 Acyl carrier protein
T20H4.5 putative NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrial
fum-1 putative fumarate hydratase, mitochondrial
vha-14 V-type proton ATPase subunit D
vha-1 V-type proton ATPase 16 kDa proteolipid subunit 1
cts-1 putative citrate synthase, mitochondrial
Y56A3A.19 Acyl carrier protein
cox-5A Cytochrome c oxidase subunit 5A, mitochondrial
T27E9.2 Cytochrome b-c1 complex subunit 6
ant-1.1 Adenine Nucleotide Translocator
pssy-2 L-serine-phosphatidylethanolamine phosphatidyltransferase
cox-6C COX6C domain-containing protein
vha-11 V-type proton ATPase subunit C
vha-3 V-type proton ATPase 16 kDa proteolipid subunit 2/3
Y69A2AR.18 Uncharacterized protein
Y69A2AR.3 Complex I-9kD
Y94H6A.8 putative NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12
vha-19 Vacuolar H ATPase
mai-2 ATPase inhibitor mai-2, mitochondrial
F29B9.11 Uncharacterized protein
cyc-2.1 Cytochrome c 2.1
C46G7.1 Uncharacterized protein
vha-8 Vacuolar H ATPase
F42G8.10 Complex I-ESSS
isp-1 Cytochrome b-c1 complex subunit Rieske, mitochondrial
vha-5 V-type proton ATPase subunit a
F49C12.12 Uncharacterized protein
vha-17 V-type proton ATPase subunit e
C33A12.1 putative NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 5
pyp-1 Inorganic pyrophosphatase 1
ard-1 Alcohol/Ribitol Dehydrogenase family
ZK809.3 Complex I-B17
kdp-1 KASH (Klarsicht/ANC-1/Syne Homology) Domain Protein
dld-1 Dihydrolipoyl dehydrogenase, mitochondrial
dlat-2 2-oxoacid_dh domain-containing protein
nuo-5 NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial
hpo-18 Uncharacterized protein
atp-4 ATP synthase-coupling factor 6, mitochondrial
tofu-2 B30.2/SPRY domain-containing protein
lpd-9 LiPid Depleted
atp-5 ATP synthase subunit d, mitochondrial
R04F11.2 ATP synthase subunit e, mitochondrial
eat-6 Sodium/potassium-transporting ATPase subunit alpha
F53F4.10 putative NADH dehydrogenase [ubiquinone] flavoprotein 2, mitochondrial
ril-1 RNAi-Induced Longevity
B0250.5 putative 3-hydroxyisobutyrate dehydrogenase, mitochondrial
F31D4.9 Complex I-MWFE
vha-15 putative V-type proton ATPase subunit H 2
immt-1 MICOS complex subunit MIC60-1
vha-12 putative V-type proton ATPase subunit B
asb-2 ATP Synthase B homolog
R07E4.3 Complex III subunit 8
asg-2 putative ATP synthase subunit g 2, mitochondrial
F46H5.3 putative arginine kinase F46H5.3
sdha-1 Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial
ucr-2.1 Ubiquinol-Cytochrome c oxidoReductase complex
vha-20 Vacuolar H ATPase
sucl-1 Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial
ucr-2.2 Peptidase_M16 domain-containing protein
nkat-3 Aminotran_1_2 domain-containing protein
gas-1 putative NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial
got-1.2 Aspartate aminotransferase, cytoplasmic
C23G10.2 RutC family protein C23G10.2
nduf-6 putative NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial
crls-1 putative cardiolipin synthase (CMP-forming)
K12H4.5 Uncharacterized protein
vha-2 V-type proton ATPase 16 kDa proteolipid subunit 3
nduf-2.2 Complex I-49kD
C14B9.10 Uncharacterized protein
mev-1 Succinate dehydrogenase cytochrome b560 subunit, mitochondrial
ucr-11 Ubiquinol-Cytochrome c oxidoReductase complex
nduf-5 Complex I-15 kDa
cas-2 C-CAP/cofactor C-like domain-containing protein
vha-13 V-type proton ATPase catalytic subunit A
cox-6B Cytochrome OXidase assembly protein
cox-7C Cytochrome c oxidase polypeptide VIIc
cisd-1 ZnF_CDGSH domain-containing protein
pdha-1 Pyruvate dehydrogenase E1 component subunit alpha;putative pyruvate dehydrogenase E1 component subunit alpha, mitochondrial
tspo-1 TranSlocator PrOtein homolog
Y54G11A.17 Uncharacterized protein
oxy-5 Uncharacterized protein
nuo-3 NADH Ubiquinone Oxidoreductase
F02A9.10 putative methylcrotonoyl-CoA carboxylase beta chain, mitochondrial
Symbol Function*
ATP5F1E ATP synthase F1 subunit epsilon
NDUFA4 NDUFA4 mitochondrial complex associated
COX11 cytochrome c oxidase copper chaperone COX11
UQCRC1 ubiquinol-cytochrome c reductase core protein 1
COX7A1 cytochrome c oxidase subunit 7A1
COX5A cytochrome c oxidase subunit 5A
COX6B1 cytochrome c oxidase subunit 6B
ATP6V1H ATPase H+ transporting V1 subunit H
NDUFB2 NADH:ubiquinone oxidoreductase subunit B2
NDUFB10 NADH:ubiquinone oxidoreductase subunit B10
SLC25A5 solute carrier family 25 member 5
APOOL apolipoprotein O like
SLC25A3 solute carrier family 25 member 3
COX4I1 cytochrome c oxidase subunit 4I1
ATP6V1C1 ATPase H+ transporting V1 subunit C1
SUCLG1 succinate-CoA ligase GDP/ADP-forming subunit alpha
LHPP phospholysine phosphohistidine inorganic pyrophosphate phosphatase
PPA2 inorganic pyrophosphatase 2
NDUFA1 NADH:ubiquinone oxidoreductase subunit A1
MDH1 malate dehydrogenase 1
GATB glutamyl-tRNA amidotransferase subunit B
MGST3 microsomal glutathione S-transferase 3
HINT2 histidine triad nucleotide binding protein 2
COX19 COX19 cytochrome c oxidase assembly homolog (S. cerevisiae)
HIGD2A HIG1 hypoxia inducible domain family member 2A
LOC696956 cytochrome c oxidase subunit 6A1, mitochondrial
IMMT inner membrane mitochondrial protein
NDUFC1 NADH:ubiquinone oxidoreductase subunit C1
SSR4 signal sequence receptor subunit 4
NDUFA10 NADH:ubiquinone oxidoreductase subunit A10
APRT adenine phosphoribosyltransferase
NDUFA2 NADH:ubiquinone oxidoreductase subunit A2
NDUFB1 NADH:ubiquinone oxidoreductase subunit B1
NDUFA11 NADH:ubiquinone oxidoreductase subunit A11
ATP5MC1 ATP synthase membrane subunit c locus 1
UQCRC2 ubiquinol-cytochrome c reductase core protein II
COPS9 COP9 signalosome subunit 9
ATP5ME ATP synthase membrane subunit e
ATP6V0D1 ATPase H+ transporting V0 subunit d1
ATP5PO ATP synthase peripheral stalk subunit OSCP
IDH3G isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit gamma
DBI diazepam binding inhibitor, acyl-CoA binding protein
NDUFA8 NADH:ubiquinone oxidoreductase subunit A8
MPC2 mitochondrial pyruvate carrier 2
TXNL4A thioredoxin like 4A
ENY2 ENY2 transcription and export complex 2 subunit
PIN4 peptidylprolyl cis/trans isomerase, NIMA-interacting 4
CHCHD7 coiled-coil-helix-coiled-coil-helix domain containing 7
SDHB succinate dehydrogenase complex iron sulfur subunit B
ATP5MG ATP synthase membrane subunit g
LOC700087 cytochrome b-c1 complex subunit Rieske, mitochondrial
SRP9 signal recognition particle 9
RNASEH2C ribonuclease H2 subunit C
ATP5PD ATP synthase peripheral stalk subunit d
CYC1 cytochrome c1
NDUFAB1 NADH:ubiquinone oxidoreductase subunit AB1
POLR2L RNA polymerase II, I and III subunit L
UQCRB ubiquinol-cytochrome c reductase binding protein
ATP5F1A ATP synthase F1 subunit alpha
ATP5MJ ATP synthase membrane subunit j
MRPL32 mitochondrial ribosomal protein L32
ATP6V1F ATPase H+ transporting V1 subunit F
ATP6V0B ATPase H+ transporting V0 subunit b
GHITM growth hormone inducible transmembrane protein
TMEM126B transmembrane protein 126B
AIFM1 apoptosis inducing factor mitochondria associated 1
MRPL33 mitochondrial ribosomal protein L33
TMEM126A transmembrane protein 126A
ATP5MC3 ATP synthase membrane subunit c locus 3
CHCHD2 coiled-coil-helix-coiled-coil-helix domain containing 2
ATP6V1G1 ATPase H+ transporting V1 subunit G1
ATP5MC2 ATP synthase membrane subunit c locus 2
ATP5PB ATP synthase peripheral stalk-membrane subunit b
NDUFS4 NADH:ubiquinone oxidoreductase subunit S4
VDAC2 voltage dependent anion channel 2
MRPS36 mitochondrial ribosomal protein S36
COQ9 coenzyme Q9
NDUFB6 NADH:ubiquinone oxidoreductase subunit B6
LOC705178 cytochrome b-c1 complex subunit Rieske, mitochondrial
TUFM Tu translation elongation factor, mitochondrial
ATP6V1B2 ATPase H+ transporting V1 subunit B2
ATP5F1D ATP synthase F1 subunit delta
NDUFB11 NADH:ubiquinone oxidoreductase subunit B11
NDUFV2 NADH:ubiquinone oxidoreductase core subunit V2
COX7B cytochrome c oxidase subunit 7B
MMUT methylmalonyl-CoA mutase
CHCHD1 coiled-coil-helix-coiled-coil-helix domain containing 1
PGK1 phosphoglycerate kinase 1
FAM174C family with sequence similarity 174 member C
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
LOC707227 cytochrome c oxidase subunit 5B, mitochondrial
MRPS16 mitochondrial ribosomal protein S16
BLOC1S1 biogenesis of lysosomal organelles complex 1 subunit 1
TMEM219 transmembrane protein 219
ETFA electron transfer flavoprotein subunit alpha
BOLA3 bolA family member 3
GOT2 glutamic-oxaloacetic transaminase 2
UQCRH ubiquinol-cytochrome c reductase hinge protein
POLDIP2 DNA polymerase delta interacting protein 2
SDHA succinate dehydrogenase complex flavoprotein subunit A
UQCR ubiquinol-cytochrome c reductase, 6.4kDa subunit
GOT1 glutamic-oxaloacetic transaminase 1
PET100 PET100 cytochrome c oxidase chaperone
NDUFB5 NADH:ubiquinone oxidoreductase subunit B5
UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
NDUFS6 NADH:ubiquinone oxidoreductase subunit S6
NDUFA6 NADH:ubiquinone oxidoreductase subunit A6
ATP6V1A ATPase H+ transporting V1 subunit A
VDAC1 voltage dependent anion channel 1
TMA7 translation machinery associated 7 homolog
NDUFB8 NADH:ubiquinone oxidoreductase subunit B8
NDUFS8 NADH:ubiquinone oxidoreductase core subunit S8
LOC710937 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 3 pseudogene
UBL5 ubiquitin like 5
PPARGC1B PPARG coactivator 1 beta
PIN1 peptidylprolyl cis/trans isomerase, NIMA-interacting 1
NDUFA7 NADH:ubiquinone oxidoreductase subunit A7
LOC711326 succinate dehydrogenase complex, subunit D, integral membrane protein
ROMO1 reactive oxygen species modulator 1
NDUFB9 NADH:ubiquinone oxidoreductase subunit B9
NDUFV1 NADH:ubiquinone oxidoreductase core subunit V1
CCDC56 coiled-coil domain containing 56
RPAIN RPA interacting protein
NDUFA12 NADH:ubiquinone oxidoreductase subunit A12
OXA1L OXA1L mitochondrial inner membrane protein
MRPL52 mitochondrial ribosomal protein L52
TXN thioredoxin
COX17 cytochrome c oxidase copper chaperone COX17
NDUFS3 NADH:ubiquinone oxidoreductase core subunit S3
ATP5F1B ATP synthase F1 subunit beta
NDUFB4 NADH:ubiquinone oxidoreductase subunit B4
ATP5F1C ATP synthase F1 subunit gamma
FOXRED1 FAD dependent oxidoreductase domain containing 1
MRPL12 mitochondrial ribosomal protein L12
BZW2 basic leucine zipper and W2 domains 2
ECSIT ECSIT signaling integrator
TIMM17B translocase of inner mitochondrial membrane 17B
SNRPD2 small nuclear ribonucleoprotein D2 polypeptide
TMEM256 transmembrane protein 256
C7H15orf61 chromosome 7 C15orf61 homolog
SAMM50 SAMM50 sorting and assembly machinery component
MRPL42 mitochondrial ribosomal protein L42
NEDD8 NEDD8 ubiquitin like modifier
NAA38 N-alpha-acetyltransferase 38, NatC auxiliary subunit
NDUFA13 NADH:ubiquinone oxidoreductase subunit A13
IDH3B isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit beta
DMAC1 distal membrane arm assembly component 1
ATP5IF1 ATP synthase inhibitory factor subunit 1
PCCB propionyl-CoA carboxylase subunit beta
NDUFB7 NADH:ubiquinone oxidoreductase subunit B7
LOC717879 cytochrome c oxidase subunit 7A2, mitochondrial
COX8A cytochrome c oxidase subunit 8A
MRPL48 mitochondrial ribosomal protein L48
COX10 cytochrome c oxidase assembly factor heme A:farnesyltransferase COX10
ANAPC15 anaphase promoting complex subunit 15
UQCC3 ubiquinol-cytochrome c reductase complex assembly factor 3
PRDX5 peroxiredoxin 5
NDUFS2 NADH:ubiquinone oxidoreductase core subunit S2
MDH2 malate dehydrogenase 2
CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10
LOC720636 cytochrome b-c1 complex subunit 9
NDUFS7 NADH:ubiquinone oxidoreductase core subunit S7
SPAG7 sperm associated antigen 7
PHPT1 phosphohistidine phosphatase 1
GSTP1 glutathione S-transferase pi 1
NDUFA9 NADH:ubiquinone oxidoreductase subunit A9
SURF1 SURF1 cytochrome c oxidase assembly factor
NDUFV3 NADH:ubiquinone oxidoreductase subunit V3
ACOT13 acyl-CoA thioesterase 13
PDHA1 pyruvate dehydrogenase E1 subunit alpha 1
CYCS cytochrome c, somatic
TXN2 thioredoxin 2
UQCC2 ubiquinol-cytochrome c reductase complex assembly factor 2
NDUFC2 NADH:ubiquinone oxidoreductase subunit C2
CHURC1 churchill domain containing 1
COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
COX6C cytochrome c oxidase subunit 6C
ATP5MK ATP synthase membrane subunit k
COX14 uncharacterized protein C12orf62-like
NDUFA5 NADH:ubiquinone oxidoreductase subunit A5
TMEM258 transmembrane protein 258
LOC106993126 uncharacterized LOC106993126
NDUFA3 NADH:ubiquinone oxidoreductase subunit A3
NAA10 N-alpha-acetyltransferase 10, NatA catalytic subunit
ATP6AP1 ATPase H+ transporting accessory protein 1
LOC106996230 cytochrome b-c1 complex subunit 2, mitochondrial pseudogene
MICOS10 mitochondrial contact site and cristae organizing system subunit 10
ATP5MF ATP synthase membrane subunit f
LOC106998836 cytochrome c oxidase subunit 7C, mitochondrial
SLIRP SRA stem-loop interacting RNA binding protein
LOC114669847 NADH dehydrogenase [ubiquinone] iron-sulfur protein 5
MRPL21 mitochondrial ribosomal protein L21
AFG3L2 AFG3 like matrix AAA peptidase subunit 2
Symbol Function*
PLA2G15 phospholipase A2 group XV
ATP5F1B ATP synthase F1 subunit beta
ATP6V0E1 ATPase H+ transporting V0 subunit e1
SAMM50 SAMM50 sorting and assembly machinery component
NDUFA6 NADH:ubiquinone oxidoreductase subunit A6
ACO2 aconitase 2
TXN2 thioredoxin 2
COX5B cytochrome c oxidase subunit 5B
MDH1 malate dehydrogenase 1
HINT1 histidine triad nucleotide binding protein 1
DMAC1 distal membrane arm assembly component 1
CUTA cutA divalent cation tolerance homolog
ATP6V1C1 ATPase H+ transporting V1 subunit C1
NDUFB9 NADH:ubiquinone oxidoreductase subunit B9
CYC1 cytochrome c1
ATP6V1F ATPase H+ transporting V1 subunit F
NDUFA5 NADH:ubiquinone oxidoreductase subunit A5
CYCS cytochrome c, somatic
SNX10 sorting nexin 10
NDUFS5 NADH:ubiquinone oxidoreductase subunit S5
UROD uroporphyrinogen decarboxylase
NDUFA12 NADH:ubiquinone oxidoreductase subunit A12
SLC25A3 solute carrier family 25 member 3
SLC4A2 solute carrier family 4 member 2
MTCH2 mitochondrial carrier 2
NDUFS3 NADH:ubiquinone oxidoreductase core subunit S3
NDUFV1 NADH:ubiquinone oxidoreductase core subunit V1
PRDX5 peroxiredoxin 5
COX8A cytochrome c oxidase subunit VIIIA (ubiquitous)
PSENEN presenilin enhancer, gamma-secretase subunit
UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
NDUFA13 NADH:ubiquinone oxidoreductase subunit A13
COPE COPI coat complex subunit epsilon
NDUFB7 NADH:ubiquinone oxidoreductase subunit B7
TECR trans-2,3-enoyl-CoA reductase
GADD45GIP1 GADD45G interacting protein 1
NDUFA7 NADH:ubiquinone oxidoreductase subunit A7
NDUFA11 NADH:ubiquinone oxidoreductase subunit A11
MICOS13 mitochondrial contact site and cristae organizing system subunit 13
NDUFS7 NADH:ubiquinone oxidoreductase core subunit S7
ATP5F1D ATP synthase F1 subunit delta
NDUFC2 NADH:ubiquinone oxidoreductase subunit C2
IDH3B isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit beta
ROMO1 reactive oxygen species modulator 1
LOC477508 cytochrome c oxidase subunit 6A1, mitochondrial
CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10
NDUFA9 NADH:ubiquinone oxidoreductase subunit A9
C27H12orf4 chromosome 27 C12orf4 homolog
ATP6V1E1 ATPase H+ transporting V1 subunit E1
COX15 cytochrome c oxidase assembly homolog COX15
NDUFB8 NADH:ubiquinone oxidoreductase subunit B8
MRPL43 mitochondrial ribosomal protein L43
ATP5F1C ATP synthase F1 subunit gamma
NDUFA2 NADH:ubiquinone oxidoreductase subunit A2
GOT2 glutamic-oxaloacetic transaminase 2
COQ9 coenzyme Q9
AK2 adenylate kinase 2
ATP5IF1 ATP synthase inhibitory factor subunit 1
SDHB succinate dehydrogenase complex iron sulfur subunit B
CIAO2A cytosolic iron-sulfur assembly component 2A
COX5A cytochrome c oxidase subunit Va
ATP5PO ATP synthase peripheral stalk subunit OSCP
NDUFV3 NADH:ubiquinone oxidoreductase subunit V3
PPA2 inorganic pyrophosphatase 2
NDUFB4 NADH:ubiquinone oxidoreductase subunit B4
NCBP2 nuclear cap binding protein subunit 2
NDUFS6 NADH:ubiquinone oxidoreductase subunit S6
SDHA succinate dehydrogenase complex flavoprotein subunit A
NDUFB5 NADH:ubiquinone oxidoreductase subunit B5
ATP5MC3 ATP synthase membrane subunit c locus 3
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
GLRX2 glutaredoxin 2
DCAF8 DDB1 and CUL4 associated factor 8
PEX19 peroxisomal biogenesis factor 19
NIT1 nitrilase 1
NDUFS2 NADH:ubiquinone oxidoreductase core subunit S2
SDHC succinate dehydrogenase complex subunit C
VDAC2 voltage dependent anion channel 2
HIGD2A HIG1 hypoxia inducible domain family member 2A
NDUFS4 NADH:ubiquinone oxidoreductase subunit S4
MOCS2 molybdenum cofactor synthesis 2
SDHD succinate dehydrogenase complex subunit D
TRAPPC2L trafficking protein particle complex subunit 2L
COX4I1 cytochrome c oxidase subunit 4I1
EMC8 ER membrane protein complex subunit 8
ATP6V0D1 ATPase H+ transporting V0 subunit d1
CHCHD2 coiled-coil-helix-coiled-coil-helix domain containing 2
NDUFAB1 NADH:ubiquinone oxidoreductase subunit AB1
UQCRC2 ubiquinol-cytochrome c reductase core protein 2
COQ7 coenzyme Q7, hydroxylase
ATP6V0C ATPase H+ transporting V0 subunit c
NDUFB10 NADH:ubiquinone oxidoreductase subunit B10
LAMTOR5 late endosomal/lysosomal adaptor, MAPK and MTOR activator 5
MRPS14 mitochondrial ribosomal protein S14
MPC2 mitochondrial pyruvate carrier 2
ATP5F1A ATP synthase F1 subunit alpha
NDUFV2 NADH:ubiquinone oxidoreductase core subunit V2
OXA1L OXA1L mitochondrial inner membrane protein
NEDD8 NEDD8 ubiquitin like modifier
ATP6V1D ATPase H+ transporting V1 subunit D
NME2 non-metastatic cells 2, protein (NM23B) expressed in
NDUFA8 NADH:ubiquinone oxidoreductase subunit A8
HCCS holocytochrome c synthase
NDUFB11 NADH:ubiquinone oxidoreductase subunit B11
HSD17B10 hydroxysteroid 17-beta dehydrogenase 10
MRPL13 mitochondrial ribosomal protein L13
ATP6V0B ATPase H+ transporting V0 subunit b
TCIRG1 T cell immune regulator 1, ATPase H+ transporting V0 subunit a3
TRPT1 tRNA phosphotransferase 1
PIN1 peptidylprolyl cis/trans isomerase, NIMA-interacting 1
TRAPPC5 trafficking protein particle complex subunit 5
SMPD1 sphingomyelin phosphodiesterase 1
SUCLA2 succinate-CoA ligase ADP-forming subunit beta
ATP6V1B2 ATPase H+ transporting V1 subunit B2
UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X
TIGAR TP53 induced glycolysis regulatory phosphatase
LOC486776 mitochondrial import inner membrane translocase subunit Tim23
GOT1 glutamic-oxaloacetic transaminase 1
LHPP phospholysine phosphohistidine inorganic pyrophosphate phosphatase
ATP6V1H ATPase H+ transporting V1 subunit H
ATP6V1A ATPase H+ transporting V1 subunit A
MRPL36 mitochondrial ribosomal protein L36
PPARGC1B PPARG coactivator 1 beta
COQ6 coenzyme Q6, monooxygenase
ATP5MC1 ATP synthase membrane subunit c locus 1
SLC25A5 solute carrier family 25 member 5
COX17 cytochrome c oxidase copper chaperone COX17
ACP1 acid phosphatase 1
PFDN1 prefoldin subunit 1
RNASEK ribonuclease K
CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3
HADHB hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
NDUFC1 NADH:ubiquinone oxidoreductase subunit C1
NDUFA10 NADH:ubiquinone oxidoreductase subunit A10
UQCRC1 ubiquinol-cytochrome c reductase core protein 1
UQCRH ubiquinol-cytochrome c reductase hinge protein
SEM1 SEM1 26S proteasome subunit
MPC1 mitochondrial pyruvate carrier 1
COX11 cytochrome c oxidase copper chaperone COX11
SMDT1 single-pass membrane protein with aspartate rich tail 1
UQCRQ ubiquinol-cytochrome c reductase complex III subunit VII
TOMM40L translocase of outer mitochondrial membrane 40 like
PCBD2 pterin-4 alpha-carbinolamine dehydratase 2
MRPL34 mitochondrial ribosomal protein L34
SDHAF3 succinate dehydrogenase complex assembly factor 3
NDUFS8 NADH:ubiquinone oxidoreductase core subunit S8
ALKBH7 alkB homolog 7
CLPP caseinolytic mitochondrial matrix peptidase proteolytic subunit
UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI
POLR2E RNA polymerase II, I and III subunit E
LSM7 LSM7 homolog, U6 small nuclear RNA and mRNA degradation associated
GLRX5 glutaredoxin 5
ATP6V1G1 ATPase H+ transporting V1 subunit G1
COX7A1 cytochrome c oxidase subunit 7A1
LOC612644 cytochrome c oxidase subunit 6B1
MICOS10 mitochondrial contact site and cristae organizing system subunit 10
FMC1 formation of mitochondrial complex V assembly factor 1 homolog
ATP5MK ATP synthase membrane subunit k
ATP5MJ ATP synthase membrane subunit j
NDUFB2 NADH:ubiquinone oxidoreductase subunit B2
CCDC127 coiled-coil domain containing 127
LOC100684983 cytochrome c oxidase subunit 7B, mitochondrial
C15H12orf73 chromosome 15 C12orf73 homolog
PSMB7 proteasome 20S subunit beta 7
NDUFB6 NADH:ubiquinone oxidoreductase subunit B6
ATP5MG ATP synthase membrane subunit g
MRPL44 mitochondrial ribosomal protein L44
NDUFB3 NADH:ubiquinone oxidoreductase subunit B3
DNAJC19 DnaJ heat shock protein family (Hsp40) member C19
EMC6 ER membrane protein complex subunit 6
NDUFA4 NDUFA4 mitochondrial complex associated
SMIM4 small integral membrane protein 4
HSBP1 heat shock factor binding protein 1
HADHA hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
LOC102152234 V-type proton ATPase subunit e 1-like
ATP5F1E ATP synthase F1 subunit epsilon
NDUFA1 NADH:ubiquinone oxidoreductase subunit A1
LOC102157225 uncharacterized LOC102157225
LOC106558651 uncharacterized LOC106558651
POLR2L RNA polymerase II, I and III subunit L
FAM174C family with sequence similarity 174 member C
GPX4 glutathione peroxidase 4
LOC119866325 cytochrome c oxidase subunit 6B1-like
LOC119866751 cytochrome b-c1 complex subunit 7
ATP5PF ATP synthase peripheral stalk subunit F6
UBL4A ubiquitin like 4A
ATP6AP1 ATPase H+ transporting accessory protein 1
LOC119870484 ATP synthase subunit d, mitochondrial
NUDT16L1 nudix hydrolase 16 like 1
NDUFB1 NADH:ubiquinone oxidoreductase subunit B1
TOMM5 translocase of outer mitochondrial membrane 5
Symbol Function*
MIC10 Mic10p
MIC19 Mic19p
QCR6 ubiquinol--cytochrome-c reductase subunit 6
YMR31 mitochondrial 37S ribosomal protein YMR31
SDH2 succinate dehydrogenase iron-sulfur protein subunit SDH2
COX12 cytochrome c oxidase subunit VIb
SHH4 protein SHH4
ATP14 F1F0 ATP synthase subunit h
COX8 cytochrome c oxidase subunit VIII
VMA6 H(+)-transporting V0 sector ATPase subunit d
VMA1 H(+)-transporting V1 sector ATPase subunit A
INH1 ATPase inhibitor
SUB2 ATP-dependent RNA helicase SUB2
COX9 cytochrome c oxidase subunit VIIa
ATP16 F1F0 ATP synthase subunit delta
SDH4 succinate dehydrogenase membrane anchor subunit SDH4
ATP5 F1F0 ATP synthase subunit 5
TIM11 F1F0 ATP synthase subunit e
ATP17 F1F0 ATP synthase subunit f
QCR7 ubiquinol--cytochrome-c reductase subunit 7
ATP1 F1F0 ATP synthase subunit alpha
COR1 ubiquinol--cytochrome-c reductase subunit COR1
PET9 ADP/ATP carrier protein PET9
IPP1 inorganic diphosphatase IPP1
ATP3 F1F0 ATP synthase subunit gamma
VMA2 H(+)-transporting V1 sector ATPase subunit B
GUS1 glutamate--tRNA ligase GUS1
COX13 cytochrome c oxidase subunit VIa
COX4 cytochrome c oxidase subunit IV
VMA7 H(+)-transporting V1 sector ATPase subunit F
VOA1 Voa1p
MRPS35 mitochondrial 37S ribosomal protein MRPS35
QCR9 ubiquinol--cytochrome-c reductase subunit 9
NCE101 Nce101p
QCR8 ubiquinol--cytochrome-c reductase subunit 8
GSM1 Gsm1p
CYC1 cytochrome c isoform 1
MIR1 Mir1p
AIM24 Aim24p
ATP2 F1F0 ATP synthase subunit beta
MCR1 cytochrome-b5 reductase
SDH1 succinate dehydrogenase flavoprotein subunit SDH1
SDH3 succinate dehydrogenase cytochrome b subunit SDH3
VMA5 H(+)-transporting V1 sector ATPase subunit C
ATP7 F1F0 ATP synthase subunit d
MIC60 Mic60p
ATP19 F1F0 ATP synthase subunit k
YNG1 Yng1p
CYT1 ubiquinol--cytochrome-c reductase catalytic subunit CYT1
VPH1 H(+)-transporting V0 sector ATPase subunit a
VMA4 H(+)-transporting V1 sector ATPase subunit E
KGD1 alpha-ketoglutarate dehydrogenase KGD1
ATP18 F1F0 ATP synthase subunit i
NDI1 NADH-ubiquinone reductase (H(+)-translocating) NDI1
SHH3 protein SHH3
NDE1 NADH-ubiquinone reductase (H(+)-translocating) NDE1
COX7 cytochrome c oxidase subunit VII
PPA2 inorganic diphosphatase PPA2
COX5A cytochrome c oxidase subunit Va
VMA11 H(+)-transporting V0 sector ATPase subunit c'
ATP15 F1F0 ATP synthase subunit epsilon
COX10 protoheme IX farnesyltransferase
ODC1 mitochondrial 2-oxodicarboxylate carrier
COX11 Cox11p
ATP4 F1F0 ATP synthase subunit 4
PMA2 H(+)-exporting P2-type ATPase PMA2
ATP20 F1F0 ATP synthase subunit g
VMA13 H(+)-transporting V1 sector ATPase subunit H
QCR2 ubiquinol--cytochrome-c reductase subunit 2
QCR10 ubiquinol--cytochrome-c reductase subunit 10
VMA16 H(+)-transporting V0 sector ATPase subunit c''
VMA10 H(+)-transporting V1 sector ATPase subunit G
COX6 cytochrome c oxidase subunit VI
VMA8 H(+)-transporting V1 sector ATPase subunit D
VMA3 H(+)-transporting V0 sector ATPase subunit c
RIP1 ubiquinol--cytochrome-c reductase catalytic subunit RIP1
VMA9 H(+)-transporting V0 sector ATPase subunit e
MIN8 Min8p
YPR170W-B uncharacterized protein
Symbol Function*
cox13 putative cytochrome c oxidase subunit VIa
cox12 putative cytochrome c oxidase subunit VIb
cox5 putative cytochrome c oxidase subunit V
qcr2 putative ubiquinol-cytochrome-c reductase complex core protein Qcr2
cox9 putative cytochrome c oxidase subunit VIIa
sdh3 succinate dehydrogenase cytochrome B subunit
cyc1 putative cytochrome c
qcr9 putative ubiquinol-cytochrome-c reductase complex subunit 9
atp5 putative F0-ATPase delta subunit atp5
fum1 putative fumarate hydratase
qcr7 putative ubiquinol-cytochrome-c reductase complex subunit 6
SPCC70.02c putative ATPase inhibitor
vma8 putative V-type ATPase V1 subunit D
atp17 putative F0-ATPase subunit F
SPBC1703.13c putative inorganic phosphate transporter
atp4 putative F0-ATPase subunit atp4
atp3 putative F1-ATPase gamma subunit atp3
tim11 putative F0-ATPase subunit E
qcr6 putative ubiquinol-cytochrome-c reductase complex subunit 8
vma10 putative V-type ATPase V1 domain subunit G
atp16 putative F1-ATPase delta subunit atp16
SPBC83.13 putative tricarboxylic acid transporter
atp15 putative F0-ATPase epsilon subunit atp15
atp7 putative F0-ATPase subunit D
cyt1 putative cytochrome c1 Cyt1
SPBC25H2.09 hypothetical protein
atp14 putative F1-ATPase subunit H
lsm5 putative U6 snRNP-associated protein Lsm5
anc1 adenine nucleotide carrier Anc1
SPBC36.10 putative protein sorting protein
vma7 putative V-type ATPase V1 subunit F
SPBC3E7.05c crista junction-formation protein
SPBC8D2.12c putative cytochrome C oxidase subunit I translational activator
sdh4 TIM22 inner membrane protein import complex anchor subunit Tim18
qcr1 putative MPP complex beta subunit Qcr1
qcr10 putative ubiquinol-cytochrome-c reductase complex subunit Qcr10
SPAC24C9.02c putative cytochrome c1 heme lyase
atp1 F1-ATPase alpha subunit
azr1 serine/threonine protein phosphatase Azr1
vma1 V-type ATPase V1 domain-containing subunit A
sdh1 putative succinate dehydrogenase Sdh1
vma11 putative V-type ATPase V0 proteolipid subunit vma11
atp20 putative F0-ATPase subunit G
vma13 putative V-type ATPase V1 subunit H
atp18 putative F0-ATPase subunit J
atp2 F1-ATPase beta subunit Atp2
SPAC26A3.14c hypothetical protein
lsm6 putative U6 snRNP-associated protein Lsm6
vma16 putative V-type ATPase V0 subunit c''
tsr3 putative SSU-rRNA maturation protein Tsr3
SPAC16E8.04c putative chorismate mutase
phb1 putative prohibitin Phb1
qcr8 ubiquinol-cytochrome-c reductase complex subunit 7
SPAC1687.17c putative Der1 family protein
erg5 C-22 sterol desaturase Erg5
vma3 V-type ATPase V0 subunit c (proteolipid subunit)
cox6 putative cytochrome c oxidase subunit VI
SPAC1B3.20 hypothetical protein
cox8 putative cytochrome c oxidase subunit VIII
acp1 F-actin-capping protein alpha subunit
sdh2 succinate dehydrogenase iron-sulfur subunit protein
SPAC1486.01 putative manganese superoxide dismutase
SPAC3A12.02 putative inorganic diphosphatase
vma4 putative V-type ATPase V1 subunit E
cox4 putative cytochrome c oxidase subunit IV
cdc42 Rho family GTPase Cdc42
SPAPJ691.03 hypothetical protein
vma2 V-type ATPase V1 subunit B
vma5 putative V-type ATPase V1 subunit C
pop8 putative RNase P and RNase MRP subunit Pop8
vma9 putative V-type ATPase V0 subunit e
SPBC29A3.21 hypothetical protein
atp19 putative F0-ATPase subunit K
cox7 putative cytochrome c oxidase subunit VII Cox7
coa2 putative cytochrome C oxidase assembly factor Coa2
Symbol Function*
MDH1 malate dehydrogenase 1
SDHB succinate dehydrogenase complex iron sulfur subunit B
SDHA succinate dehydrogenase complex flavoprotein subunit A
UROS uroporphyrinogen III synthase
ATP5F1C ATP synthase F1 subunit gamma
NDUFV2 NADH:ubiquinone oxidoreductase core subunit V2
LOC101080736 NADH dehydrogenase [ubiquinone] 1 subunit C2
COX17 cytochrome c oxidase copper chaperone COX17
CHCHD2 coiled-coil-helix-coiled-coil-helix domain containing 2
AAMDC adipogenesis associated Mth938 domain containing
NDUFA12 NADH:ubiquinone oxidoreductase subunit A12
MRPL48 mitochondrial ribosomal protein L48
NDUFA3 NADH:ubiquinone oxidoreductase subunit A3
LOC101081808 cytochrome c oxidase subunit 5A, mitochondrial
ATP6V1E1 ATPase H+ transporting V1 subunit E1
ATP6V1F ATPase H+ transporting V1 subunit F
IDH2 isocitrate dehydrogenase (NADP(+)) 2
NDUFB2 NADH:ubiquinone oxidoreductase subunit B2
GLRX5 glutaredoxin 5
NAA20 N-alpha-acetyltransferase 20, NatB catalytic subunit
NDUFB10 NADH:ubiquinone oxidoreductase subunit B10
SMDT1 single-pass membrane protein with aspartate rich tail 1
COX7A1 cytochrome c oxidase subunit 7A1
TBCA tubulin folding cofactor A
ATP6V1C1 ATPase H+ transporting V1 subunit C1
NDUFA6 NADH:ubiquinone oxidoreductase subunit A6
CB4H12orf73 chromosome B4 C12orf73 homolog
ATP6V0B ATPase H+ transporting V0 subunit b
NDUFV3 NADH:ubiquinone oxidoreductase subunit V3
MDH2 malate dehydrogenase 2
PSMA7 proteasome 20S subunit alpha 7
PPA2 inorganic pyrophosphatase 2
HCCS holocytochrome c synthase
SLC25A3 solute carrier family 25 member 3
COQ9 coenzyme Q9
ATP5F1D ATP synthase F1 subunit delta
LOC101085531 cytochrome c oxidase subunit 7B, mitochondrial
NDUFA1 NADH:ubiquinone oxidoreductase subunit A1
IDH3A isocitrate dehydrogenase (NAD(+)) 3 catalytic subunit alpha
NDUFB9 NADH:ubiquinone oxidoreductase subunit B9
COQ7 coenzyme Q7, hydroxylase
ATP5IF1 ATP synthase inhibitory factor subunit 1
MRPS36 mitochondrial ribosomal protein S36
LOC101086703 cytochrome b-c1 complex subunit 10
ATP5MK ATP synthase membrane subunit k
NDUFB1 NADH:ubiquinone oxidoreductase subunit B1
MRPL30 mitochondrial ribosomal protein L30
ATP5F1B ATP synthase F1 subunit beta
ATP5PO ATP synthase peripheral stalk subunit OSCP
SAMM50 SAMM50 sorting and assembly machinery component
SDHC succinate dehydrogenase complex subunit C
IMMT inner membrane mitochondrial protein
NDUFS2 NADH:ubiquinone oxidoreductase core subunit S2
CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10
MRPL12 mitochondrial ribosomal protein L12
OXA1L OXA1L mitochondrial inner membrane protein
CD3H18orf32 chromosome D3 C18orf32 homolog
NDUFB4 NADH:ubiquinone oxidoreductase subunit B4
NDUFS4 NADH:ubiquinone oxidoreductase subunit S4
UQCRC1 ubiquinol-cytochrome c reductase core protein 1
ATP6AP2 ATPase H+ transporting accessory protein 2
LOC101089914 cytochrome c oxidase subunit 4 isoform 1, mitochondrial
ATP5MG ATP synthase membrane subunit g
TIMM10 translocase of inner mitochondrial membrane 10
NDUFAF6 NADH:ubiquinone oxidoreductase complex assembly factor 6
NDUFB5 NADH:ubiquinone oxidoreductase subunit B5
LOC101090590 cytochrome b-c1 complex subunit 7
COX5B cytochrome c oxidase subunit 5B
NDUFA7 NADH:ubiquinone oxidoreductase subunit A7
MRPS28 mitochondrial ribosomal protein S28
NDUFA8 NADH:ubiquinone oxidoreductase subunit A8
NDUFB8 NADH:ubiquinone oxidoreductase subunit B8
NDUFC1 NADH:ubiquinone oxidoreductase subunit C1
ATP6V1A ATPase H+ transporting V1 subunit A
COX10 cytochrome c oxidase assembly factor heme A:farnesyltransferase COX10
ATP6AP1 ATPase H+ transporting accessory protein 1
GATD3A glutamine amidotransferase class 1 domain containing 3A
NDUFB7 NADH:ubiquinone oxidoreductase subunit B7
COX7A2L cytochrome c oxidase subunit 7A2 like
NDUFA5 NADH:ubiquinone oxidoreductase subunit A5
ATP6V1B2 ATPase H+ transporting V1 subunit B2
VDAC2 voltage dependent anion channel 2
NDUFA9 NADH:ubiquinone oxidoreductase subunit A9
GRINA glutamate ionotropic receptor NMDA type subunit associated protein 1
NDUFB3 NADH:ubiquinone oxidoreductase subunit B3
NDUFV1 NADH:ubiquinone oxidoreductase core subunit V1
COX7A2 cytochrome c oxidase subunit 7A2
UQCC2 ubiquinol-cytochrome c reductase complex assembly factor 2
NDUFA11 NADH:ubiquinone oxidoreductase subunit A11
DLD dihydrolipoamide dehydrogenase
CYC1 cytochrome c1
LOC101094311 cytochrome b-c1 complex subunit Rieske, mitochondrial
NDUFS8 NADH:ubiquinone oxidoreductase core subunit S8
RNASEK ribonuclease K
MRPL33 mitochondrial ribosomal protein L33
ATP5ME ATP synthase membrane subunit e
NDUFS5 NADH:ubiquinone oxidoreductase subunit S5
LOC101095032 cytochrome b-c1 complex subunit 6, mitochondrial
ATP6V1H ATPase H+ transporting V1 subunit H
SDHD succinate dehydrogenase complex subunit D
LOC101095773 cytochrome c oxidase subunit 6A1, mitochondrial
PDLIM1 PDZ and LIM domain 1
ATP6V0A1 ATPase H+ transporting V0 subunit a1
NDUFA2 NADH:ubiquinone oxidoreductase subunit A2
NDUFS7 NADH:ubiquinone oxidoreductase core subunit S7
COX8A cytochrome c oxidase subunit 8A
NDUFB6 NADH:ubiquinone oxidoreductase subunit B6
UQCRQ ubiquinol-cytochrome c reductase complex III subunit VII
LOC101096876 cytochrome c oxidase subunit 6C
NDUFS3 NADH:ubiquinone oxidoreductase core subunit S3
ATP5PB ATP synthase peripheral stalk-membrane subunit b
ATP5MC3 ATP synthase membrane subunit c locus 3
ATP5MC1 ATP synthase membrane subunit c locus 1
CDIPT CDP-diacylglycerol--inositol 3-phosphatidyltransferase
RRAGA Ras related GTP binding A
ATP5PD ATP synthase peripheral stalk subunit d
NDUFB11 NADH:ubiquinone oxidoreductase subunit B11
LOC101098213 cytochrome c
PHPT1 phosphohistidine phosphatase 1
NDUFAB1 NADH:ubiquinone oxidoreductase subunit AB1
IDH3B isocitrate dehydrogenase (NAD(+)) 3 non-catalytic subunit beta
MRPS7 mitochondrial ribosomal protein S7
MIEF2 mitochondrial elongation factor 2
ECSIT ECSIT signaling integrator
SNX10 sorting nexin 10
BOLA3 bolA family member 3
ESRRA estrogen related receptor alpha
ATP5PF ATP synthase peripheral stalk subunit F6
ATP5MJ ATP synthase membrane subunit j
NDUFA4 NDUFA4 mitochondrial complex associated
JTB jumping translocation breakpoint
NDUFA13 NADH:ubiquinone oxidoreductase subunit A13
LOC101100266 cytochrome c oxidase subunit 6B1
PDHB pyruvate dehydrogenase E1 subunit beta
ATP5MC2 ATP synthase membrane subunit c locus 2
CMC2 C-X9-C motif containing 2
ATP6V0D1 ATPase H+ transporting V0 subunit d1
NDUFAF2 NADH:ubiquinone oxidoreductase complex assembly factor 2
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
NDUFS6 NADH:ubiquinone oxidoreductase subunit S6
ACO2 aconitase 2
ATP6V0C ATPase H+ transporting V0 subunit c
ATP5F1A ATP synthase F1 subunit alpha
UQCRC2 ubiquinol-cytochrome c reductase core protein 2
LOC102899183 cytochrome c oxidase subunit 7C, mitochondrial
TOMM7 translocase of outer mitochondrial membrane 7
COPS9 COP9 signalosome subunit 9
LOC102902265 uncharacterized protein LINC00116 homolog
ATP5MF ATP synthase membrane subunit f
ATP5F1E ATP synthase F1 subunit epsilon
UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X
SMIM20 small integral membrane protein 20
LOC111559796 small integral membrane protein 26-like


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